학술논문


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'학술논문' 에서 검색결과 540건 | 목록 1~20
Academic Journal
Genet Med
NIHR BioResource Rare Diseases Consortium 2019, 'Analysis of 51 proposed hypertrophic cardiomyopathy genes from genome sequencing data in sarcomere negative cases has negligible diagnostic yield', Genetics in medicine : official journal of the American College of Medical Genetics, vol. 21, no. 7, pp. 1576-1584. https://doi.org/10.1038/s41436-018-0375-z
Academic Journal
Am J Med Genet A
Fasham, J, Arno, G, Lin, S, Xu, M, Carss, K J, Hull, S, Lane, A, Robson, A G, Wenger, O, Self, J E, Harlalka, G V, Salter, C G, Schema, L, Moss, T J, Cheetham, M E, Moore, A T, Raymond, F L, Chen, R, Baple, E L, Webster, A R & Crosby, A H 2019, ' Delineating the expanding phenotype associated with SCAPER gene mutation ', American Journal of Medical Genetics Part A, vol. 179, no. 8, pp. 1665-1671 . https://doi.org/10.1002/ajmg.a.61202
American Journal of Medical Genetics Part A, vol 179, iss 8
Academic Journal
Westbury, S K, Canault, M, Greene, D, Bermejo, E, Hanlon, K, Lambert, M P, Millar, C M, Nurden, P, Obaji, S G, Revel-Vilk, S, Van Geet, C, Downes, K, Papadia, S, Tuna, S, Watt, C, Consortium, N B-R D, Freson, K, Laffan, M A, Ouwehand, W H, Alessi, M-C, Turro, E & Mumford, A D 2017, 'Expanded repertoire of RASGRP2 variants responsible for platelet dysfunction and severe bleeding', Blood, vol. 130, no. 8. https://doi.org/10.1182/blood-2017-03-776773
Academic Journal
Carss, Keren JArno, GavinErwood, MarieStephens, JonathanSanchis-Juan, AlbaHull, SarahMegy, KarynGrozeva, DetelinaDewhurst, EleanorMalka, SamanthaPlagnol, VincentPenkett, ChristopherStirrups, KathleenRizzo, RobertaWright, GenevieveJosifova, DraganaBitner-Glindzicz, MariaScott, Richard HClement, EmmaAllen, LouiseArmstrong, RuthBrady, Angela FCarmichael, JennyChitre, ManaliHenderson, Robert HHHurst, JaneMacLaren, Robert EMurphy, ElainePaterson, JoanRosser, ElisabethThompson, Dorothy AWakeling, EmmaOuwehand, Willem HMichaelides, MichelMoore, Anthony TConsortium, NIHR-BioResource Rare DiseasesAitman, TimothyAlachkar, HanaAli, SoniaAllsup, DavidAmbegaonkar, GautumAnderson, JulieAntrobus, RichardArumugakani, GururajAshford, SofieAstle, WilliamAttwood, AntonyAustin, SteveBacchelli, ChiaraBakchoul, TamamBariana, Tadbir KBaxendale, HelenBennett, DavidBethune, ClaireBibi, ShahnazBleda, MartaBoggard, HarmBolton-Maggs, PaulaBooth, ClaireBradley, John RBrady, AngieBrown, MatthewBrowning, MichaelBryson, ChristineBurns, SiobhanCalleja, PaulCanham, NatalieCarss, KerenCaulfield, MarkChalmers, ElizabethChandra, AnitaChinnery, PatrickChurch, ColinClements-Brod, NaomiClowes, VirginiaCoghlan, GerryCollins, PeterCooper, NicholaCreaser-Myers, AmandaDaCosta, RosaDaugherty, LouiseDavies, SophieDavis, JohnDe Vries, MinkaDeegan, PatrickDeevi, Sri VVDeshpande, CharuDevlin, LisaDoffinger, RainerDormand, NatalieDrewe, ElizabethEdgar, David
American Journal of Human Genetics, vol 100, iss 1
Academic Journal
Rhodes, CJBatai, KBleda, MHaimel, MSouthgate, LGermain, MPauciulo, MWHadinnapola, CAman, JGirerd, BArora, ARobbins, IRoden, DMRosenzweig, EBSaydain, GScelsi, LSchilz, RSeeger, WShaffer, CMSimms, RWSimon, MWalter, RESitbon, OSuntharalingam, JTang, HTchourbanov, AYThenappan, TTorres, FToshner, MRTreacy, CMNoordegraaf, AVWaisfisz, QWharton, JWalsworth, AKWhite, RJWilt, JWort, SJYung, DLawrie, AHumbert, MSoubrier, FTrégouët, D-AKnight, JProkopenko, IKittles, RGräf, SNichols, WCTrembath, RCDesai, AAMorrell, NWWilkins, MRUK NIHR BioResource Rare Diseases ConsortiumUK PAH Cohort Study ConsortiumHanscombe, KBUS PAH Biobank ConsortiumKarnes, JHKaakinen, MGall, HUlrich, AHarbaum, LCebola, IFerrer, JLutz, KSwietlik, EMAhmad, FAmouyel, PArcher, SLArgula, RAustin, EDBadesch, DBakshi, SBarnett, CBenza, RBhatt, NBogaard, HJBurger, CDChakinala, MChurch, CCoghlan, JGCondliffe, RCorris, PADanesino, CDebette, SElliott, CGElwing, JEyries, MFortin, TFranke, AFrantz, RPFrost, AGarcia, JGNGhio, SGhofrani, H-AGibbs, JSRHarley, JHe, HHill, NSHirsch, RHouweling, ACHoward, LSIvy, DKiely, DGKlinger, JKovacs, GLahm, TLaudes, MMachado, RDRoss, RVMMarsolo, KMartin, LJMoledina, SMontani, DNathan, SDNewnham, MOlschewski, AOlschewski, HOudiz, RJOuwehand, WHPeacock, AJPepke-Zaba, JRehman, Z
Academic Journal
Carss, Keren J.Arno, GavinErwood, MarieStephens, JonathanSanchis Juan, AlbaHull, SarahMegy, KarynGrozeva, DetelinaDewhurst, EleanorMalka, SamanthaPlagnol, VincentPenkett, ChristopherStirrups, KathleenRizzo, RobertaWright, GenevieveJosifova, DraganaBitner Glindzicz, MariaScott, Richard H.Clement, EmmaAllen, LouiseArmstrong, RuthBrady, Angela F.Carmichael, JennyChitre, ManaliHenderson, Robert H. H.Hurst, JaneMaclaren, Robert E.Murphy, ElainePaterson, JoanRosser, ElisabethThompson, Dorothy A.Wakeling, EmmaOuwehand, Willem H.Michaelides, MichelMoore, Anthony T.Aitman, TimothyAlachkar, HanaAli, SoniaAllsup, DavidAmbegaonkar, GautumAnderson, JulieAntrobus, RichardArumugakani, GururajAshford, SofieAstle, WilliamAttwood, AntonyAustin, SteveBacchelli, ChiaraBakchoul, TamamBariana, Tadbir K.Baxendale, HelenBennett, DavidBethune, ClaireBibi, ShahnazBleda, MartaBoggard, HarmBolton Maggs, PaulaBooth, ClaireBradley, John R.Brady, AngieBrown, MatthewBrowning, MichaelBryson, ChristineBurns, SiobhanCalleja, PaulCanham, NatalieCarss, KerenCaulfield, MarkChalmers, ElizabethChandra, AnitaChinnery, PatrickChurch, ColinClements Brod, NaomiClowes, VirginiaCoghlan, GerryCollins, PeterCooper, NicholaCreaser Myers, AmandaDacosta, RosaDaugherty, LouiseDavies, SophieDavis, JohnDe Vries, MinkaDeegan, PatrickDeevi, Sri V. V.Deshpande, CharuDevlin, LisaDoffinger, RainerDormand, NatalieDrewe, ElizabethEdgar, DavidEgner, WilliamErber, Wendy N.Everington, TamaraFavier, RemiFirth, HelenFletcher, DebraFlinter, FrancesFox, James C.Frary, AmyFreson, KathleenFurie, BruceFurnell, AbigailGale, DanielGardham, AliceGattens, MichaelGhali, NeetiGhataorhe, Pavandeep K.Ghurye, RohitGibbs, SimonGilmour, KimberleyGissen, PaulGoddard, SarahGomez, KeithGordins, PavelGräf, StefanGreene, DanielGreenhalgh, AlanGreinacher, AndreasGrigoriadou, SofiaHackett, ScottHadinnapola, CharakaHague, RosieHaimel, MatthiasHalmagyi, CsabaHammerton, TraceyHart, DanielHayman, GrantHeemskerk, Johan W. M.Henderson, RobertHensiek, AnkeHenskens, YvonneHerwadkar, ArchanaHolden, SimonHolder, MurielHolder, SusanHu, FengyuanHuissoon, AarnoudHumbert, MarcJames, RogerJolles, StephenKazmi, RashidKeeling, DavidKelleher, PeterKelly, Anne M.Kennedy, FionaKiely, DavidKingston, NathalieKoziell, AniaKrishnakumar, DeepaKuijpers, Taco W.Kumararatne, DinakanthaKurian, ManjuLaffan, Michael A.Lambert, Michele P.Allen, Hana LangoLawrie, AllanLear, SaraLees, MelissaLentaigne, ClaireLiesner, RiLinger, RachelLonghurst, HilaryLorenzo, LorenaMachado, RajivMackenzie, RobMaclaren, RobertMaher, EamonnMaimaris, JesmeenMangles, SarahManson, AniaMapeta, RutendoMarkus, Hugh S.Martin, JenniferMasati, LarahmieMathias, MaryMatser, VeraMaw, AnnaMcdermott, ElizabethMcjannet, ColeenMeacham, StuartMeehan, SharonMehta, SarjuMillar, Carolyn M.Moledina, ShahinMoore, AnthonyMorrell, NicholasMumford, AndrewMurng, SaiNejentsev, SergeyNoorani, SadiaNurden, PaquitaOksenhendler, EricPapadia, SofiaPark, Soo MiParker, AlasdairPasi, JohnPatch, ChrisPayne, JeanettePeacock, AndrewPeerlinck, KathelijnePenkett, Christopher J.Pepke Zaba, JoannaPerry, David J.Pollock, ValPolwarth, GaryPonsford, MarkQasim, WaseemQUINTI, IsabellaRankin, StuartRankin, JuliaRaymond, F. LucyRehnstrom, KarolaReid, EvanRhodes, Christopher J.Richards, MichaelRichardson, SylviaRichter, AlexRoberts, IreneRondina, MatthewRoughley, CatherineRue Albrecht, KevinSamarghitean, CrinaSandford, RichardSantra, SaikatSargur, RavishankarSavic, SinisaSchulman, SolSchulze, HaraldScott, RichardScully, MarieSeneviratne, SuranjithSewell, CarrockShamardina, OlgaShipley, DebbieSimeoni, IleniaSivapalaratnam, SutheshSmith, KennethSohal, AmanSouthgate, LauraStaines, SimonStaples, EmilyStauss, HansStein, PenelopeStock, SophieSuntharalingam, JayTait, R. CampbellTalks, KateTan, YvonneThachil, JeckoThaventhiran, JamesThomas, EllenThomas, MoiraThompson, DorothyThrasher, AdrianTischkowitz, MarcTitterton, CatherineToh, Cheng HockToshner, MarkTreacy, CarmenTrembath, RichardTuna, SalihTurek, WojciechTurro, ErnestVan Geet, ChrisVeltman, MarijkeVogt, Julievon Ziegenweldt, JulieNoordegraaf, Anton VonkWanjiku, IvyWarner, Timothy Q.Wassmer, EvangelineWatkins, HughWebster, AndrewWelch, SteveWestbury, SarahWharton, JohnWhitehorn, DeborahWilkins, MartinWillcocks, LisaWilliamson, CatherineWoods, GeoffreyWort, JohnYeatman, NigelYong, PatrickYoung, TimYu, PingWebster, Andrew R.
NIHR BioResource Rare Diseases Consortium 2017, 'Comprehensive Rare Variant Analysis via Whole-Genome Sequencing to Determine the Molecular Pathology of Inherited Retinal Disease', American journal of human genetics, vol. 100, no. 1, pp. 75-90. https://doi.org/10.1016/j.ajhg.2016.12.003
Carss, K J, Arno, G, Erwood, M, Stephens, J, Sanchis-Juan, A, Hull, S, Megy, K, Grozeva, D, Dewhurst, E, Malka, S, Plagnol, V, Penkett, C, Stirrups, K, Rizzo, R, Wright, G, Josifova, D, Bitner-Glindzicz, M, Scott, R H, Clement, E, Allen, L, Armstrong, R, Brady, A F, Carmichael, J, Chitre, M, Henderson, R H H, Hurst, J, MacLaren, R E, Murphy, E, Paterson, J, Rosser, E, Thompson, D A, Wakeling, E, Ouwehand, W H, Michaelides, M, Moore, A T, Webster, A R, Raymond, F L & Westbury, S 2017, 'Comprehensive Rare Variant Analysis via Whole-Genome Sequencing to Determine the Molecular Pathology of Inherited Retinal Disease', American Journal of Human Genetics, vol. 100, no. 1, pp. 75-90. https://doi.org/10.1016/j.ajhg.2016.12.003
Academic Journal
Am J Respir Crit Care Med
Repositorio Institucional de la Consejería de Sanidad de la Comunidad de Madrid
Consejería de Sanidad de la Comunidad de Madrid
NIHR BioResource for Translational Research-Rare Diseases32, National Cohort Study of Idiopathic and Heritable PAH33 & PAH Biobank Enrolling Centers' Investigators33 2022, 'First Genotype-Phenotype Study in TBX4 Syndrome Gain-of-Function Mutations Causative for Lung Disease', American Journal of Respiratory and Critical Care Medicine, vol. 206, no. 12, pp. 1522-1533. https://doi.org/10.1164/rccm.202203-0485OC
American journal of respiratory and critical care medicine, Vol. 206, no.12, p. 1522-1533 (2022)
Academic Journal
Whitworth, JSmith, PSMartin, J-EWest, HLuchetti, ARodger, FClark, GCarss, KStephens, JStirrups, KPenkett, CMapeta, RAshford, SMegy, KShakeel, HAhmed, MAdlard, JBarwell, JBrewer, CCasey, RTArmstrong, RCole, TEvans, DGFostira, FGreenhalgh, LHanson, HHenderson, AHoffman, JIzatt, LKumar, AKwong, ALalloo, FOng, KRPaterson, JPark, S-MChen-Shtoyerman, RSearle, CSide, LSkytte, A-BSnape, KWoodward, ERTischkowitz, MDMaher, ERAitman, TAlachkar, HAli, SAllen, LAllsup, DAmbegaonkar, GAnderson, JAntrobus, RArno, GArumugakani, GAstle, WAttwood, AAustin, SBacchelli, CBakchoul, TBariana, TKBaxendale, HBennett, DBethune, CBibi, SBitner-Glindzicz, MBleda, MBoggard, HBolton-Maggs, PBooth, CBradley, JRBrady, ABrown, MBrowning, MBryson, CBurns, SCalleja, PCanham, NCarmichael, JCaulfield, MChalmers, EChandra, AChinnery, PChitre, MChurch, CClement, EClements-Brod, NClowes, VCoghlan, GCollins, PCookson, VCooper, NCorris, PCreaser-Myers, ADacosta, RDaugherty, LDavies, SDavis, JDe Vries, MDeegan, PDeevi, SVVDeshpande, CDevlin, LDewhurst, EDixon, PDoffinger, RDormand, NDrewe, EEdgar, DEgner, WErber, WNErwood, MEverington, TFavier, RFirth, HFletcher, DFlinter, FFrary, AFreson, KFurie, BFurnell, AGale, DGardham, AGattens, MGhali, NGhataorhe, PKGhurye, RGibbs, SGilmour, KGissen, PGoddard, SGomez, KGordins, PGraf, SGräf, SGreene, DGreenhalgh, AGreinacher, AGrigoriadou, SGrozeva, DHackett, SHadinnapola, CHague, RHaimel, MHalmagyi, CHammerton, THart, DHayman, GHeemskerk, JWMHenderson, RHensiek, AHenskens, YHerwadkar, AHolden, SHolder, MHolder, SHu, FVeld, AHuissoon, AHumbert, MHurst, JJames, RJolles, SJosifova, DKazmi, RKeeling, DKelleher, PKelly, AMKennedy, FKiely, DKingston, NKoziell, AKrishnakumar, DKuijpers, TWKuijpers, TKumararatne, DKurian, MLaffan, MALambert, MPAllen, HLLango-Allen, HLawrie, ALear, SLees, MLentaigne, CLiesner, RLinger, RLonghurst, HLorenzo, LLouka, EMachado, RRoss, RMMaclaren, RMaher, EMaimaris, JMangles, SManson, AMarkus, HSMartin, JMasati, LMathias, MMatser, VMaw, AMcDermott, EMcJannet, CMeacham, SMeehan, SMehta, SMichaelides, MMillar, CMMoledina, SMoore, AMorrell, NMumford, AMurng, SMurphy, ENejentsev, SNoorani, SNurden, POksenhendler, EOthman, SOuwehand, WHPapadia, SParker, APasi, JPatch, CPayne, JPeacock, APeerlinck, KPenkett, CJPepke-Zaba, JPerry, DPerry, DJPollock, VPolwarth, GPonsford, MQasim, WQuinti, IRankin, SRankin, JRaymond, FLRayner-Matthews, PRehnstrom, KReid, ERhodes, CJRichards, MRichardson, SRichter, ARoberts, IRondina, MRosser, ERoughley, CRoy, NRue-Albrecht, KSamarghitean, CSanchis-Juan, ASandford, RSantra, SSargur, RSavic, SSchotte, GSchulman, SSchulze, HScott, RScully, MSeneviratne, SSewell, CShamardina, OShipley, DSimeoni, ISivapalaratnam, SSmith, KGCSohal, ASouthgate, LStaines, SStaples, EStark, HStauss, HStein, PStock, SSuntharalingam, JTalks, KTan, YThachil, JThaventhiran, JThomas, EThomas, MThompson, DThrasher, ATischkowitz, MTitterton, CToh, C-HToshner, MTreacy, CTrembath, RTuna, STurek, WTurro, EVan Geet, CVeltman, MVogt, JVon Ziegenweldt, JNoordegraaf, AVWakeling, EWanjiku, IWarner, TQWassmer, EWatkins, HWatt, CWebster, NWelch, SWestbury, SWharton, JWhitehorn, DWilkins, MWillcocks, LWilliamson, CWoods, GWort, JYeatman, NYong, PYoung, TYu, P
Am J Hum Genet
AMERICAN JOURNAL OF HUMAN GENETICS
NIHR BioResource Rare Diseases Consortium 2018, 'Comprehensive Cancer-Predisposition Gene Testing in an Adult Multiple Primary Tumor Series Shows a Broad Range of Deleterious Variants and Atypical Tumor Phenotypes', American journal of human genetics, vol. 103, no. 1, pp. 3-18. https://doi.org/10.1016/j.ajhg.2018.04.013
Whitworth, J, Smith, P S, Martin, J-E, West, H, Luchetti, A, Rodger, F, Clark, G, Carss, K, Stephens, J, Stirrups, K, Penkett, C, Mapeta, R, Ashford, S, Megy, K, Shakeel, H, Ahmed, M, Adlard, J, Barwell, J, Brewer, C, Casey, R T, Armstrong, R, Cole, T, Evans, D G, Fostira, F, Greenhalgh, L, Hanson, H, Henderson, A, Hoffman, J, Izatt, L, Kumar, A, Kwong, A, Lalloo, F, Ong, K R, Paterson, J, Park, S-M, Chen-Shtoyerman, R, Searle, C, Side, L, Skytte, A-B, Snape, K, Woodward, E R & NIHR BioResource Rare Diseases Consortium 2018, 'Comprehensive Cancer-Predisposition Gene Testing in an Adult Multiple Primary Tumor Series Shows a Broad Range of Deleterious Variants and Atypical Tumor Phenotypes', American Journal of Human Genetics, vol. 103, no. 1, pp. 3-18. https://doi.org/10.1016/j.ajhg.2018.04.013
2018, 'Comprehensive Cancer-Predisposition Gene Testing in an Adult Multiple Primary Tumor Series Shows a Broad Range of Deleterious Variants and Atypical Tumor Phenotypes', American Journal of Human Genetics, vol. 103, no. 1, pp. 3-18. https://doi.org/10.1016/j.ajhg.2018.04.013
2018, ' Comprehensive Cancer-Predisposition Gene Testing in an Adult Multiple Primary Tumor Series Shows a Broad Range of Deleterious Variants and Atypical Tumor Phenotypes ', American Journal of Human Genetics, vol. 103, no. 1, pp. 3-18 . https://doi.org/10.1016/j.ajhg.2018.04.013
NIHR BioResource Rare Diseases Consortium & Evans, D G 2018, 'Comprehensive Cancer-Predisposition Gene Testing in an Adult Multiple Primary Tumor Series Shows a Broad Range of Deleterious Variants and Atypical Tumor Phenotypes', Cell, vol. 103, no. 1. https://doi.org/10.1016/j.ajhg.2018.04.013
American Journal of Human Genetics
Academic Journal
Rhodes, Christopher JBatai, KenBleda, MartaHaimel, MatthiasSouthgate, LauraGermain, MarinePauciulo, Michael WHadinnapola, CharakaAman, JurjanGirerd, BarbaraArora, AmitKnight, JoHanscombe, Ken BKarnes, Jason HKaakinen, MarikaGall, HenningUlrich, AnnaHarbaum, LarsCebola, InêsFerrer, JorgeConsortium, The NIHR BioResourceRare Diseases Consortium UK PAH Cohort Study Consortium and the US PAH BiobankAhmad, FerhaanAmouyel, PhilippeL., Archer StephenArgula, RahulD., Austin EricBadesch, DavidBakshi, SahilBarnett, Christopher FBenza, RaymondBhatt, NitinBogaard, Harm JBurger, Charles DChakinala, Murali MChurch, ColinCoghlan, John GCondliffe, RobinCorris, Paul ADanesino, CesareDebette, StéphanieElliott, C GregoryElwing, JeanEyries, MelanieFortin, TerryFranke, AndreFrantz, Robert PFrost, AdaaniGarcia, Joe GNGhio, StefanoGhofrani, Hossein-ArdeschirSimon, JGibbs, RHarley, John BHe, HuaHill, Nicholas SHirsch, RusselHouweling, Arjan CHoward, Luke SIvy, DunbarKiely, David GKlinger, JamesKovacs, GaborLahm, TimLaudes, MatthiasLutz, KatieMachado, Rajiv DRoss, Robert V MacKenzieMarsolo, KeithMartin, Lisa JMoledina, ShahinMontani, DavidNathan, Steven DNewnham, MichaelOlschewski, AndreaOlschewski, HorstOudiz, Ronald JOuwehand, Willem HPeacock, Andrew JPepke-Zaba, JoannaRehman, ZiaRobbins, Ivan MRoden, Dan MRosenzweig, Erika BSaydain, GhulamScelsi, LauraSchilz, RobertSeeger, WernerShaffer, Christian MSimms, Robert WSimon, MarcSitbon, OlivierSuntharalingam, JaySwietlik, EmiliaTang, HaiyangTchourbanov, Alexander YThenappan, ThenappanTorres, FernandoToshner, Mark RTreacy, Carmen MNoordegraaf, Anton VonkWaisfisz, QuintenWalsworth, Anna KWalter, Robert EWharton, JohnWhite, R JamesWilt, JeffreyWort, Stephen JYung, DelphineLawrie, AllanHumbert, MarcSoubrier, FlorentTrégouët, David-AlexandreProkopenko, IngaKittles, RichardGräf, StefanNichols, William CTrembath, Richard CDesai, Ankit AMorrell, Nicholas WWilkins, Martin R
Academic Journal
Hadinnapola, CharakaBleda, MartaHaimel, MatthiasScreaton, NicholasSwift, AndrewDorfmüller, PeterPreston, Stephen DSouthwood, MarkHernandez-Sanchez, JulesMartin, JenniferTreacy, CarmenYates, KatherineBogaard, HarmChurch, ColinCoghlan, GerryCondliffe, RobinCorris, Paul AGibbs, SimonGirerd, BarbaraHolden, SimonHumbert, MarcKiely, David GLawrie, AllanMachado, RajivMacKenzie Ross, RobertMoledina, ShahinMontani, DavidNewnham, MichaelPeacock, AndrewPepke-Zaba, JoannaRayner-Matthews, PaulaShamardina, OlgaSoubrier, FlorentSouthgate, LauraSuntharalingam, JayToshner, MarkTrembath, RichardNoordegraaf, Anton VonkWilkins, Martin RWort, Stephen JWharton, JohnGräf, StefanMorrell, Nicholas WAitman, TimothyBennett, DavidCaulfield, MarkChinnery, PatrickGale, DanielKoziell, AniaKuijpers, Taco WLaffan, Michael AMaher, EamonnMarkus, Hugh SOuwehand, Willem HPerry, DavidRaymond, F LucyRoberts, IreneSmith, KennethThrasher, AdrianWatkins, HughWilliamson, CatherineWoods, GeoffreyAshford, SofieBradley, John RFletcher, DebraHammerton, TraceyJames, RogerKingston, NathaliePenkett, Christopher JStirrups, KathleenVeltman, MarijkeYoung, TimBrown, MatthewClements-Brod, NaomiDavis, JohnDewhurst, EleanorErwood, MarieFrary, AmyLinger, RachelPapadia, SofiaRehnstrom, KarolaStark, HannahAllsup, DavidAustin, SteveBakchoul, TamamBariana, Tadbir KBolton-Maggs, PaulaChalmers, ElizabethCollins, PeterErber, Wendy NEverington, TamaraFavier, RemiFreson, KathleenFurie, BruceGattens, MichaelGomez, KeithGreene, DanielGreinacher, AndreasHart, DanielHeemskerk, Johan WMHenskens, YvonneKazmi, RashidKeeling, DavidKelly, Anne MLambert, Michele PLentaigne, ClaireLiesner, RiMangles, SarahMathias, MaryMillar, Carolyn MMumford, AndrewNurden, PaquitaPayne, JeanettePasi, JohnPerry, David JPeerlinck, KathelijneRichards, MichaelRondina, MatthewRoughley, CatherineSchulman, SolSchulze, HaraldScully, MarieSivapalaratnam, SutheshTait, R CampbellTalks, KateThachil, JeckoTurro, ErnestToh, Cheng-HockVan Geet, ChrisDe Vries, MinkaWarner, Timothy QWestbury, SarahFurnell, AbigailMapeta, RutendoSimeoni, IleniaStaines, SimonStephens, JonathanWhitehorn, DeborahWatt, ChristopherAttwood, AntonyDaugherty, LouiseDeevi, SriHalmagyi, CsabaHu, FengyuanMatser, VeraMeacham, StuartMegy, KarynTitterton, CatherineTuna, SalihYu, PingVon Ziegenweldt, JulieAstle, WilliamCarss, KerenLango-Allen, HanaRichardson, SylviaCalleja, PaulRankin, StuartTurek, WojciechBryson, ChristineAnderson, JulieMcJannet, ColeenStock, SophieWassmer, EvangelineSohal, AmanSantra, SaikatVogt, JulieChitre, ManaliKrishnakumar, DeepaAmbegaonkar, GautumMaw, AnnaArmstrong, RuthPark, Soo-MiMehta, SarjuPaterson, JoanCarmichael, JennyAllen, LouiseHensiek, AnkeFirth, HelenStein, PenelopeDeegan, PatrickDoffinger, RainerParker, AlasdairBitner-Glindzicz, MariaScott, RichardHurst, JaneRosser, ElisabethLees, MelissaClement, EmmaHenderson, RobertThompson, DorothyGardham, AliceGissen, PaulJosifova, DraganaThomas, EllenPatch, ChrisDeshpande, CharuFlinter, FrancesHolder, MurielCanham, NatalieWakeling, EmmaHolder, SusanGhali, NeetiBrady, AngieClowes, VirginiaMacLaren, RobertWebster, AndrewMoore, AnthonyArno, GavinMichaelides, MichelRankin, JuliaKurian, ManjuMurphy, ElaineSanchis-Juan, AlbaGrozeva, DetelinaReid, EvanWoods, GeoffTischkowitz, MarcSandford, RichardAli, SoniaCreaser-Myers, AmandaCookson, VictoriaDaCosta, RosaDormand, NatalieGhataorhe, Pavandeep KGreenhalgh, AlanHuis In’t Veld, AnnaKennedy, FionaMackenzie Ross, RobMasati, LarahmieMeehan, SharonOthman, ShokriPollock, ValPolwarth, GaryRhodes, Christopher JRue-Albrecht, KevinSchotte, GwenShipley, DebbieTan, YvonneWanjiku, IvyWort, JohnKuijpers, TacoThaventhiran, JamesLango Allen, HanaStaples, EmilySamarghitean, CrinaAlachkar, HanaAntrobus, RichardArumugakani, GururajBacchelli, ChiaraBaxendale, HelenBethune, ClaireBibi, ShahnazBooth, ClaireBrowning, MichaelBurns, SiobhanChandra, AnitaCooper, NicholaDavies, SophieDevlin, LisaDrewe, ElizabethEdgar, DavidEgner, WilliamGhurye, RohitGilmour, KimberleyGoddard, SarahGordins, PavelGrigoriadou, SofiaHackett, ScottHague, RosieHayman, GrantHerwadkar, ArchanaHuissoon, AarnoudJolles, StephenKelleher, PeterKumararatne, DinakanthaLear, SaraLonghurst, HilaryLorenzo, LorenaMaimaris, JesmeenManson, AniaMcDermott, ElizabethMurng, SaiNejentsev, SergeyNoorani, SadiaOksenhendler, EricPonsford, MarkQasim, WaseemQuinti, IsabellaRichter, AlexSargur, RavishankarSavic, SinisaSeneviratne, SuranjithSewell, CarrockStauss, HansThomas, MoiraWelch, SteveWillcocks, LisaYeatman, NigelYong, Patrick
Hadinnapola, C, Bleda, M, Haimel, M, Screaton, N, Swift, A, Dorfmüller, P, Preston, S D, Southwood, M, Hernandez-Sanchez, J, Martin, J, Treacy, C, Yates, K, Bogaard, H, Church, C, Coghlan, G, Condliffe, R, Corris, P A, Gibbs, S, Girerd, B, Holden, S, Humbert, M, Kiely, D G, Lawrie, A, Machado, R, MacKenzie Ross, R, Moledina, S, Montani, D, Newnham, M, Peacock, A, Pepke-Zaba, J, Rayner-Matthews, P, Shamardina, O, Soubrier, F, Southgate, L, Suntharalingam, J, Toshner, M, Trembath, R, Noordegraaf, A V, Wilkins, M R, Wort, S J, Wharton, J, Gräf, S, Morrell, N W & NIHR BioResourceRare Diseases Consortium; UK National Cohort Study of Idiopathic and Heritable PAH 2017, 'Phenotypic Characterization of EIF2AK4 Mutation Carriers in a Large Cohort of Patients Diagnosed Clinically With Pulmonary Arterial Hypertension', Circulation, vol. 136, no. 21, pp. 2022-2033. https://doi.org/10.1161/CIRCULATIONAHA.117.028351
Hadinnapola, C, Bleda, M, Haimel, M, Screaton, N, Swift, A, Dorfmüller, P, Preston, S D, Southwood, M, Hernandez-Sanchez, J, Martin, J, Treacy, C, Yates, K, Bogaard, H, Church, C, Coghlan, G, Condliffe, R, Corris, P A, Gibbs, S, Girerd, B, Holden, S, Humbert, M, Kiely, D G, Lawrie, A, Machado, R, MacKenzie Ross, R, Moledina, S, Montani, D, Newnham, M, Peacock, A, Pepke-Zaba, J, Rayner-Matthews, P, Shamardina, O, Soubrier, F, Southgate, L, Suntharalingam, J, Toshner, M, Trembath, R, Noordegraaf, A V, Wilkins, M R, Wort, S J, Wharton, J, Gräf, S, Morrell, N W 2017, ' Phenotypic Characterization of EIF2AK4 Mutation Carriers in a Large Cohort of Patients Diagnosed Clinically With Pulmonary Arterial Hypertension ', Circulation, vol. 136, no. 21, pp. 2022-2033 . https://doi.org/10.1161/CIRCULATIONAHA.117.028351
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Arno, GCarss, KJHull, SZihni, CRobson, AGFiorentino, AHardcastle, AJHolder, GECheetham, MEPlagnol, VMoore, ATRaymond, FLMatter, KBalda, MSWebster, ARBlack, GHall, GIngram, SGillespie, RManson, FSergouniotis, PInglehearn, CToomes, CAli, MMcKibbin, MPoulter, JKhan, KLord, ENemeth, ADownes, SHalford, SYu, JLise, SPonitkos, NMichaelides, Mvan Heyningen, VAitman, TAlachkar, HAli, SAllen, LAllsup, DAmbegaonkar, GAnderson, JAntrobus, RArmstrong, RArumugakani, GAshford, SAstle, WAttwood, AAustin, SBacchelli, CBakchoul, TBariana, TKBaxendale, HBennett, DBethune, CBibi, SBitner-Glindzicz, MBleda, MBoggard, HBolton-Maggs, PBooth, CBradley, JRBrady, ABrown, MBrowning, MBryson, CBurns, SCalleja, PCanham, NCarmichael, JCarss, KCaulfield, MChalmers, EChandra, AChinnery, PChitre, MChurch, CClement, EClements-Brod, NClowes, VCoghlan, GCollins, PCooper, NCreaser-Myers, ADaCosta, RDaugherty, LDavies, SDavis, JDe Vries, MDeegan, PDeevi, SVVDeshpande, CDevlin, LDewhurst, EDoffinger, RDormand, NDrewe, EEdgar, DEgner, WErber, WNErwood, MEverington, TFavier, RFirth, HFletcher, DFlinter, FFox, JCFrary, AFreson, KFurie, BFurnell, AGale, DGardham, AGattens, MGhali, NGhataorhe, PKGhurye, RGibbs, SGilmour, KGissen, PGoddard, SGomez, KGordins, PGräf, SGreene, DGreenhalgh, AGreinacher, AGrigoriadou, SGrozeva, DHackett, SHadinnapola, CHague, RHaimel, MHalmagyi, CHammerton, THart, DHayman, GHeemskerk, JWMHenderson, RHensiek, AHenskens, YHerwadkar, AHolden, SHolder, MHolder, SHu, FHuissoon, AHumbert, MHurst, JJames, RJolles, SJosifova, DKazmi, RKeeling, DKelleher, PKelly, AMKennedy, FKiely, DKingston, NKoziell, AKrishnakumar, DKuijpers, TWKumararatne, DKurian, MLaffan, MALambert, MPAllen, HLLawrie, ALear, SLees, MLentaigne, CLiesner, RLinger, RLonghurst, HLorenzo, LMachado, RMackenzie, RMacLaren, RMaher, EMaimaris, JMangles, SManson, AMapeta, RMarkus, HSMartin, JMasati, LMathias, MMatser, VMaw, AMcDermott, EMcJannet, CMeacham, SMeehan, SMegy, KMehta, SMillar, CMMoledina, SMoore, AMorrell, NMumford, AMurng, SMurphy, ENejentsev, SNoorani, SNurden, POksenhendler, EOuwehand, WHPapadia, SPark, S-MParker, APasi, JPatch, CPaterson, JPayne, JPeacock, APeerlinck, KPenkett, CJPepke-Zaba, JPerry, DJPollock, VPolwarth, GPonsford, MQasim, WQuinti, IRankin, SRankin, JRehnstrom, KReid, ERhodes, CJRichards, MRichardson, SRichter, ARoberts, IRondina, MRosser, ERoughley, CRue-Albrecht, KSamarghitean, CSanchis-Juan, ASandford, RSantra, SSargur, RSavic, SSchulman, SSchulze, HScott, RScully, MSeneviratne, SSewell, CShamardina, OShipley, DSimeoni, ISivapalaratnam, SSmith, KSohal, ASouthgate, LStaines, SStaples, EStauss, HStein, PStephens, JStirrups, KStock, SSuntharalingam, JTait, RCTalks, KTan, YThachil, JThaventhiran, JThomas, EThomas, MThompson, DThrasher, ATischkowitz, MTitterton, CToh, C-HToshner, MTreacy, CTrembath, RTuna, STurek, WTurro, EVan Geet, CVeltman, MVogt, Jvon Ziegenweldt, JNoordegraaf, AVWakeling, EWanjiku, IWarner, TQWassmer, EWatkins, HWebster, AWelch, SWestbury, SWharton, JWhitehorn, DWilkins, MWillcocks, LWilliamson, CWoods, GWort, JYeatman, NYong, PYoung, TYu, P
UK Inherited Retinal Disease Consortium, NIHR BioResource Rare Diseases Consortium, NIHR BioResource Rare Diseases Consortium & NIHR BioresourceRare Diseases Consortium 2017, 'Biallelic Mutation of ARHGEF18, Involved in the Determination of Epithelial Apicobasal Polarity, Causes Adult-Onset Retinal Degeneration', American journal of human genetics, vol. 100, no. 2, pp. 334-342. https://doi.org/10.1016/j.ajhg.2016.12.014
Arno, G, Carss, K J, Hull, S, Zihni, C, Robson, A G, Fiorentino, A, Hardcastle, A J, Holder, G E, Cheetham, M E, Plagnol, V, Moore, A T, Raymond, F L, Matter, K, Balda, M S, Webster, A R, Uk Inherited Retinal Disease Consortium & Black, G 2017, 'Biallelic Mutation of ARHGEF18, Involved in the Determination of Epithelial Apicobasal Polarity, Causes Adult-Onset Retinal Degeneration', American Journal of Human Genetics. https://doi.org/10.1016/j.ajhg.2016.12.014
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