학술논문
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'학술논문'
에서 검색결과 177건 | 목록
1~20
Academic Journal
White, Matthew Anthony; Crowley, Leon; Massenzio, Francesca; Li, Xingli; Niblock, Michael; Milani, Sara; Coleman, Michael Philip; Barmada, Sami J.; Sreedharan, Jemeen
Molecular Neurobiology. 63(1)
Academic Journal
Gilbert, Bensimon; P Nigel, Leigh; Timothy, Tree; Andrea, Malaspina; Christine Am, Payan; Hang-Phuong, Pham; Pieter, Klaassen; Pamela J, Shaw; Ahmad, Al Khleifat; Maria D M, Amador; Shahram, Attarian; Simon M, Bell; Stéphane, Beltran; Emilien, Bernard; William, Camu; Philippe, Corcia; Jean-Christophe, Corvol; Philippe, Couratier; Véronique, Danel; Rabab, Debs; Claude, Desnuelle; Aikaterini, Dimitriou; John, Ealing; Florence, Esselin; Marie-Céline, Fleury; George H, Gorrie; Aude-Marie, Grapperon; Adèle, Hesters; Raul, Juntas-Morales; Ivan, Kolev; Géraldine, Lautrette; Nadine, Le Forestier; Christopher J, McDermott; Nicolas, Pageot; François, Salachas; Nikhil, Sharma; Marie-Hélène, Soriani; Jemeen, Sreedharan; Juliette, Svahn; Nick, Verber; Annie, Verschueren; Ozlem, Yildiz; Carey M, Suehs; Safaa, Saker-Delye; Claudie, Muller; Christophe, Masseguin; Hana, Hajduchova; Janine, Kirby; Cecilia, Garlanda; Massimo, Locati; Henrik, Zetterberg; Bernard, Asselain; Ammar, Al-Chalabi
Scientia
Scientia. Dipòsit d'Informació Digital del Departament de Salut
instname
Bensimon, G, Leigh, P N, Tree, T, Malaspina, A, Payan, C A, Pham, H-P, Klaassen, P, Shaw, P J, Al Khleifat, A, Amador, M D M, Attarian, S, Bell, S M, Beltran, S, Bernard, E, Camu, W, Corcia, P, Corvol, J-C, Couratier, P, Danel, V, Debs, R, Desnuelle, C, Dimitriou, A, Ealing, J, Esselin, F, Fleury, M-C, Gorrie, G H, Grapperon, A-M, Hesters, A, Juntas-Morales, R, Kolev, I, Lautrette, G, Le Forestier, N, McDermott, C J, Pageot, N, Salachas, F, Sharma, N, Soriani, M-H,Sreedharan , J, Svahn, J, Verber, N, Verschueren, A, Yildiz, O, Suehs, C M, Saker-Delye, S, Muller, C, Masseguin, C, Hajduchova, H, Garlanda, C, Locati, M & Al-Chalabi, A 2025, 'Efficacy and safety of low-dose IL-2 as an add-on therapy to riluzole (MIROCALS) : a phase 2b, double-blind, randomised, placebo-controlled trial', Lancet, vol. 405, no. 10492, pp. 1837-1850. https://doi.org/10.1016/S0140-6736(25)00262-4
Scientia. Dipòsit d'Informació Digital del Departament de Salut
instname
Bensimon, G, Leigh, P N, Tree, T, Malaspina, A, Payan, C A, Pham, H-P, Klaassen, P, Shaw, P J, Al Khleifat, A, Amador, M D M, Attarian, S, Bell, S M, Beltran, S, Bernard, E, Camu, W, Corcia, P, Corvol, J-C, Couratier, P, Danel, V, Debs, R, Desnuelle, C, Dimitriou, A, Ealing, J, Esselin, F, Fleury, M-C, Gorrie, G H, Grapperon, A-M, Hesters, A, Juntas-Morales, R, Kolev, I, Lautrette, G, Le Forestier, N, McDermott, C J, Pageot, N, Salachas, F, Sharma, N, Soriani, M-H,
Academic Journal
Xueshui Guo; Ravindra Singh Prajapati; Jiyeon Chun; Insuk Byun; Kamil K. Gebis; Yi-Zhi Wang; Karen Ling; Casey Dalton; Jeff A. Blair; Anahid Hamidianjahromi; Gemma Bachmann; Frank Rigo; Paymaan Jafar-nejad; Jeffrey N. Savas; Min Jae Lee; Jemeen Sreedharan; Robert G. Kalb
Nature Communications, Vol 17, Iss 1 (2026)
Academic Journal
Dezerae Cox; Melanie Burke; Sara Milani; Matthew A White; Fergal M Waldron; Dorothea Böken; Evgeniia Lobanova; Jemeen Sreedharan; Jenna M Gregory; David Klenerman
Advanced Science.
Academic Journal
Balendra, Rubika, MRCP PhD; Sreedharan, Jemeen, MRCP PhD; Hallegger, Martina, PhD; Luisier, Raphaëlle, PhD; Lashuel, Hilal A, Prof; Gregory, Jenna M, Prof; Patani, Rickie, Prof
The Lancet Neurology. 24(5):456-470
Academic Journal
Scott, James; Crook-Rumsey, Mark; Carobin, Anna; Bilgorai, Judith; Kelly, Gillian; Sreedharan, Jemeen; Shaw, Christopher; Bashford, James
Clinical Neurophysiology. 177
Academic Journal
Han, Shunping; Utami, Rifka N.; Qin, Yue; Liam-Or, Revadee; Sreedharan, Jemeen; Davies, Jeffrey S.; Al-Jamal, Khuloud T.
Academic Journal
Camille K. Hunt; Ahmad Al Khleifat; Ella Burchill; Joerg Ederle; Ammar Al-Chalabi; Jemeen Sreedharan
Neurogenetics
Hunt, C K, Al Khleifat, A, burchill, E, Ederle, J, Al-Chalabi, A &Sreedharan , J 2021, ' Does genetic anticipation occur in familial Alexander disease? ', NEUROGENETICS, vol. 22, no. 3, pp. 215-219 . https://doi.org/10.1007/s10048-021-00642-9
Hunt, C K, Al Khleifat, A, burchill, E, Ederle, J, Al-Chalabi, A &
Academic Journal
Balendra, Rubika; Sreedharan, Jemeen; Hallegger, Martina; Luisier, Raphaelle; Lashuel, Hilal A.; Gregory, Jenna M.; Patani, Rickie
Academic Journal
Kaitlin Weskamp; Elizabeth M. Tank; Roberto Miguez; Jonathon P. McBride; Nicolás B. Gómez; Matthew White; Ziqiang Lin; Carmen Moreno Gonzalez; Andrea Serio; Jemeen Sreedharan; Sami J. Barmada
Weskamp, K, Tank, E M, Miguez, R, McBride, J P, Gómez, N B, White, M, Lin, Z, Moreno Gonzalez, C, Serio, A, Sreedharan , J & Barmada, S J 2020, ' Shortened TDP43 isoforms upregulated by neuronal hyperactivity drive TDP43 pathology in ALS ', Journal of Clinical Investigation, vol. 130, no. 3, pp. 1139-1155 . https://doi.org/10.1172/JCI130988
Academic Journal
Alison Gowland; Sarah Opie-Martin; Kirsten M. Scott; Ashley R. Jones; Puja R. Mehta; Christine J. Batts; Cathy M. Ellis; P. Nigel Leigh; Christopher E. Shaw; Jemeen Sreedharan; Ammar Al-Chalabi
Amyotroph Lateral Scler Frontotemporal Degener
Academic Journal
Matthew A White; Eosu Kim; Amanda Duffy; Robert Adalbert; Benjamin U Phillips; Owen M Peters; Jodie Stephenson; Sujeong Yang; MASSENZIO F; Ziqiang Lin; Simon Andrews; Anne Segonds-Pichon; Jake Metterville; Lisa M Saksida; Richard Mead; Richard R Ribchester; Youssef Barhomi; Thomas Serre; Michael P Coleman; Justin R Fallon; Timothy J Bussey; Robert H Brown Jr; Jemeen Sreedharan
Nat Neurosci
Brain and Mind Institute Researchers' Publications
White, M A, Kim, E, Duffy, A, Adalbert, R, Phillips, B U, Peters, O M, Stephenson, J, Yang, S, Massenzio, F, Lin, Z, Andrews, S, Segonds-Pichon, A, Metterville, J, Saksida, L M, Mead, R, Ribchester, R R, Barhomi, Y, Serre, T, Coleman, M P, Fallon, J, Bussey, T J, Brown, R H &Sreedharan , J 2018, ' TDP-43 gains function due to perturbed autoregulation in a Tardbp knock-in mouse model of ALS-FTD ', Nature Neuroscience, vol. 21, pp. 552–563 . https://doi.org/10.1038/s41593-018-0113-5
White, M A, Kim, E, Duffy, A, Adalbert, R, Phillips, B U, Peters, O M, Stephenson, J, Yang, S, Massenzio, F, Lin, Z, Andrews, S, Segonds-Pichon, A, Metterville, J, Saksida, L M, Mead, R, Ribchester, R R, Barhomi, Y, Serre, T, Coleman, M P, Fallon, J R, Bussey, T J, Brown Jr, R H &Sreedharan , J 2018, ' TDP-43 gains function due to perturbed autoregulation in a Tardbp knock-in mouse model of ALS-FTD ', Nature Neuroscience, vol. 21, no. 4, pp. 552-563 . https://doi.org/10.1038/s41593-018-0113-5
Brain and Mind Institute Researchers' Publications
White, M A, Kim, E, Duffy, A, Adalbert, R, Phillips, B U, Peters, O M, Stephenson, J, Yang, S, Massenzio, F, Lin, Z, Andrews, S, Segonds-Pichon, A, Metterville, J, Saksida, L M, Mead, R, Ribchester, R R, Barhomi, Y, Serre, T, Coleman, M P, Fallon, J, Bussey, T J, Brown, R H &
White, M A, Kim, E, Duffy, A, Adalbert, R, Phillips, B U, Peters, O M, Stephenson, J, Yang, S, Massenzio, F, Lin, Z, Andrews, S, Segonds-Pichon, A, Metterville, J, Saksida, L M, Mead, R, Ribchester, R R, Barhomi, Y, Serre, T, Coleman, M P, Fallon, J R, Bussey, T J, Brown Jr, R H &
Academic Journal
Vance, Caroline; Rogelj, Boris; Hortobágyi, Tibor; De Vos, Kurt J.; Nishimura, Agnes Lumi; Sreedharan, Jemeen; Hu, Xun; Smith, Bradley; Ruddy, Deborah; Wright, Paul; Ganesalingam, Jeban; Williams, Kelly L.; Tripathi, Vineeta; Al-Saraj, Safa; Al-Chalabi, Ammar; Leigh, P. Nigel; Blair, Ian P.; Nicholson, Garth; de Belleroche, Jackie; Gallo, Jean-Marc; Miller, Christopher C.; Shaw, Christopher E.
Science, 2009 Feb . 323(5918), 1208-1211.
Academic Journal
Sreedharan, Jemeen; Blair, Ian P.; Tripathi, Vineeta B.; Hu, Xun; Vance, Caroline; Rogelj, Boris; Ackerley, Steven; Durnall, Jennifer C.; Williams, Kelly L.; Buratti, Emanuele; Baralle, Francisco; de Belleroche, Jacqueline; Mitchell, J. Douglas; Leigh, P. Nigel; Al-Chalabi, Ammar; Miller, Christopher C.; Nicholson, Garth; Shaw, Christopher E.
Science, 2008 Mar . 319(5870), 1668-1672.
Academic Journal
Roaya Khalaf; Sarah Martin; Cathy Ellis; Rachel Burman; Jemeen Sreedharan; Christopher Shaw; P Nigel Leigh; Martin R Turner; Ammar Al-Chalabi
J Neurol Neurosurg Psychiatry
Khalaf, R, Martin, S, Ellis, C, Burman, R,Sreedharan , J, Shaw, C, Leigh, P N, Turner, M R & Al-Chalabi, A 2019, ' Relative preservation of triceps over biceps strength in upper-limb onset ALS : The ‘split elbow’ ', Journal of Neurology, Neurosurgery & Psychiatry, vol. 90, no. 7, pp. 730-733 . https://doi.org/10.1136/jnnp-2018-319894
Khalaf, R, Martin, S, Ellis, C, Burman, R,
Academic Journal
Matthew A. White; Ziqiang Lin; Eugene Kim; Christopher M. Henstridge; Emiliano Pena Altamira; Camille K. Hunt; Ella Burchill; Isobel Callaghan; Andrea Loreto; Heledd Brown-Wright; Richard Mead; Camilla Simmons; Diana Cash; Michael P. Coleman; Jemeen Sreedharan
Acta Neuropathologica Communications, Vol 7, Iss 1, Pp 1-16 (2019)
Academic Journal
Watkins, Jodie; Ghosh, Anshua; Keerie, Amy F. A.; Alix, James J. P.; Mead, Richard J.; Sreedharan, Jemeen
Scientific Reports. 11(1)
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