학술논문

Effects of rare kidney diseases on kidney failure: a longitudinal analysis of the UK National Registry of Rare Kidney Diseases (RaDaR) cohort
Document Type
Article
Author
Wong, KatiePitcher, DavidBraddon, FionaDownward, LewisSteenkamp, RethaAnnear, NicholasBarratt, JonathanBingham, CoralieChrysochou, ConstantinaCoward, Richard JGame, DavidGriffin, SianHall, MattJohnson, SallyKanigicherla, DurgaKaret Frankl, FionaKavanagh, DavidKerecuk, LarissaMaher, Eamonn RMoochhala, ShabbirPinney, JennySayer, John ASimms, RoslynSinha, SmeetaSrivastava, ShalabhTam, Frederick W KTurner, Andrew NeilWalsh, Stephen BWaters, AoifeWilson, PatriciaWong, EdwinTaylor, Christopher MarkNitsch, DorotheaSaleem, MoinBockenhauer, DetlefBramham, KateGale, Daniel PAbat, ShariroseAdalat, ShaziaAgbonmwandolor, JoyAhmad, ZubaidahAlejmi, AbdulfattahAlmasarwah, RashidAnnear, NicholasAsgari, EllieAyers, AmandaBaharani, JyotiBalasubramaniam, GowrieKpodo, FelixBansal, TarunBarratt, AlisonBarratt, JonathanBates, MeganBayne, NatalieBendle, JanetBenyon, SarahBergmann, CarstenBhandari, SunilBingham, CoralieBoddana, PreethamBond, SallyBraddon, FionaBramham, KateBranson, AngelaBrearey, StephenBrocklebank, VickyBudwal, SharanjitByrne, ConorCairns, HughCamilleri, BrianCampbell, GaryCapell, AlysCarmody, MargaretCarson, MarionCathcart, TracyCatley, ChristineCesar, KarineChan, MelanieChea, HoudaChess, JamesCheung, Chee KayChick, Katy-JaneChitalia, NihilChristian, MartinChrysochou, TinaClark, KatherineClayton, ChristopherClissold, RhianCockerill, HelenCoelho, JoshuaColby, ElizabethColclough, VivConway, EileenCook, H TerenceCook, WendyCooper, TheresaCoward, Richard JCrosbie, SarahCserep, GaborDate, AnjaliDavidson, KatherineDavies, AmandaDhaun, NeerajDhaygude, AjayDiskin, LynnDixit, AbhijitDoctolero, EuniceDorey, SuzannahDownard, LewisDrayson, MarkDreyer, GavinDutt, TinaEtuk, KufreabasiEvans, DawnFinch, JennyFlinter, FrancesFotheringham, JamesFrancis, LucyGale, Daniel PGallagher, HughGame, DavidGarcia, EvaGavrila, MaditaGear, SusieGeddes, ColinGilchrist, MarkGittus, MattGoggolidou, ParaskeviGoldsmith, ChristopherGooden, PatriciaGoodlife, AndreaGoodwin, PriyankaGrammatikopoulos, TassosGray, BarryGriffith, MeganGumus, StephGupta, SanjanaHamilton, PatrickHarper, LorraineHarris, TessHaskell, LouiseHayward, SamanthaHegde, ShivaramHendry, BruceHewins, SueHewitson, NicolaHillman, KateHiremath, MrityunjayHowson, AlexandraHtet, ZayHuish, SharonHull, RichardHumphries, AlisterHunt, David P JHunter, KarlHunter, SamanthaIjeomah-Orji, MarilynInston, NickJayne, DavidJenfa, GbemisolaJenkins, AlisonJohnson, SallyJones, Caroline AJones, ColinJones, AmandaJones, RachelKamesh, LavanyaKanigicherla, DurgaKaret Frankl, FionaKarim, MahzuzKaur, AmritKavanagh, DavidKearley, KellyKerecuk, LarissaKhwaja, ArifKing, GarryKing, GrantKislowska, EwaKlata, EdytaKokocinska, MariaLambie, MarkLawless, LauraLedson, ThomasLennon, RachelLevine, Adam PLai, Ling Wai MaggieLipkin, GrahamLovitt, GrahamLyons, PaulMabillard, HollyMackintosh, KatherineMahdi, KhalidMaher, EamonnMarchbank, Kevin JMark, Patrick BMasoud, SherryMasunda, BridgettMavani, ZainabMayfair, JakeMcAdoo, StephenMckinnell, JoannaMelhem, NabilMeyrick, SimonMoochhala, ShabbirMorgan, PutnamMorgan, AnnMuhammad, FawadMurray, ShonaNovobritskaya, KristinaOng, Albert CMOni, LouiseOsmaston, KatePadmanabhan, NealParkes, SharonPatrick, JeanPattison, JamesPaul, RinyPercival, RachelPerkins, Stephen JPersu, AlexandrePetchey, William GPickering, Matthew CPinney, JenniferPitcher, DavidPlumb, LucyPlummer, ZoePopoola, JoycePost, FrankPower, AlbertPratt, GuyPusey, CharlesRabara, RiaRabuya, MayRaju, TinaJavier, ChaddRoberts, Ian S DRoufosse, CandiceRumjon, AdamSalama, AlanSaleem, MoinSandford, RichardSandu, Kanwaljit SSarween, NadiaSayer, John ASebire, NeilSelvaskandan, HareshSharma, AsheeshSharples, Edward JSheerin, NeilShetty, HarishShroff, RukshanaSimms, RoslynSinha, ManishSinha, SmeetaSmith, KerrySmith, LaraSrivastava, ShalabhSteenkamp, RethaStott, IanStroud, KaterinaSwift, PaulineSzklarzewicz, JustynaTam, FredTan, KayTaylor, RobertTischkowitz, MarcThomas, KayTse, YincentTurnbull, AlisonTurner, A NeilTyerman, KayUsher, MirandaVenkat-Raman, GopalakrishnanWalker, AlyconWalsh, Stephen BWaters, AoifeWatt, AngelaWebster, PhilWechalekar, AshutoshWelsh, Gavin IWest, NicolWheeler, DavidWiles, KateWillcocks, LisaWilliams, AngharadWilliams, EmmaWilliams, KarenWilson, Deborah HWilson, Patricia DWinyard, PaulWong, EdwinWong, KatieWood, GrahameWoodward, EmmaWoodward, LenWoolf, AdrianWright, David
Source
The Lancet; March-April 2024, Vol. 403 Issue: 10433 p1279-1289, 11p
Subject
Language
ISSN
01406736; 1474547X
Abstract
Individuals with rare kidney diseases account for 5–10% of people with chronic kidney disease, but constitute more than 25% of patients receiving kidney replacement therapy. The National Registry of Rare Kidney Diseases (RaDaR) gathers longitudinal data from patients with these conditions, which we used to study disease progression and outcomes of death and kidney failure.