학술논문

The case of a boy with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita: a unique instance of phacomatosis pigmentovascularis
Document Type
report
Source
Anais Brasileiros de Dermatologia. June 2015 90(3)
Subject
Hemangioma
Mongolian spot
Nevus of ota
Nevus, pigmented
Port-Wine Stain
Language
English
ISSN
0365-0596
Abstract
Phacomatosis pigmentovascularis is a rare, congenital condition characterized by a combination of cutaneous melanocytic lesions and vascular malformation. We discuss an entirely unique case of Phacomatosis pigmentovascularis with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita, which may represent a heretofore undescribed variant of phacomatosis pigmentovascularis.