학술논문

Comprehensive and Integrated Genomic Characterization of Adult Soft Tissue Sarcomas
Document Type
article
Author
Network, The Cancer Genome Atlas ResearchAbeshouse, AdamAdebamowo, ClementAdebamowo, Sally NAkbani, RehanAkeredolu, TeniolaAlly, AdrianAnderson, Matthew LAnur, PavanaAppelbaum, Elizabeth LArmenia, JoshuaAuman, J ToddBailey, Matthew HBaker, LaurenceBalasundaram, MirunaBalu, SaianandBarthel, Floris PBartlett, JohnBaylin, Stephen BBehera, MadhusmitaBelyaev, DmitryBennett, JoesphBenz, ChristopherBeroukhim, RameenBirrer, MichaelBocklage, ThèréseBodenheimer, TomBoice, LoriBootwalla, Moiz SBowen, JayBowlby, ReanneBoyd, JeffBrohl, Andrew SBrooks, DeniseByers, LaurenCarlsen, RebeccaCastro, PatriciaChen, Hsiao-WeiCherniack, Andrew DChibon, FrédericChin, LyndaCho, JuokChuah, EricChudamani, SudhaCibulskis, CarrieCooper, Lee ADCope, LeslieCordes, Matthew GCrain, DanielCurley, ErinDanilova, LudmilaDao, FannyDavis, Ian JDavis, Lara EDefreitas, TimothyDelman, KeithDemchok, John ADemetri, George DDemicco, Elizabeth GDhalla, NoreenDiao, LixiaDing, LiDiSaia, PhilDottino, PeterDoyle, Leona ADrill, EstherDubina, MichaelEschbacher, JenniferFedosenko, KonstantinFelau, InaFerguson, Martin LFrazer, ScottFronick, Catrina CFulidou, VictoriaFulton, Lucinda AFulton, Robert SGabriel, Stacey BGao, JianjiongGao, QingsongGardner, JohannaGastier-Foster, Julie MGay, Carl MGehlenborg, NilsGerken, MarkGetz, GadGodwin, Andrew KGodwin, Eryn MGordienko, ElenaGrilley-Olson, Juneko EGutman, David AGutmann, David HHayes, D NeilHegde, Apurva MHeiman, David IHeins, ZacharyHelsel, CarmenHepperla, Austin JHiggins, KellyHoadley, Katherine AHobensack, Shital
Source
Cell. 171(4)
Subject
Biological Sciences
Biomedical and Clinical Sciences
Genetics
Oncology and Carcinogenesis
Cancer
Human Genome
Digestive Diseases
Rare Diseases
Adult
Aged
Aged
80 and over
Cluster Analysis
DNA Copy Number Variations
Epigenomics
Genome
Human
Genome-Wide Association Study
Humans
Middle Aged
Mutation
Sarcoma
Young Adult
Cancer Genome Atlas Research Network. Electronic address: elizabeth.demicco@sinaihealthsystem.ca
Cancer Genome Atlas Research Network
DNA methylation
The Cancer Genome Atlas
dedifferentiated liposarcoma
genomics
immune infiltration
leiomyosarcoma
molecular subtype
myxofibrosarcoma
pleomorphism
undifferentiated pleomorphic sarcoma
Medical and Health Sciences
Developmental Biology
Biological sciences
Biomedical and clinical sciences
Language
Abstract
Sarcomas are a broad family of mesenchymal malignancies exhibiting remarkable histologic diversity. We describe the multi-platform molecular landscape of 206 adult soft tissue sarcomas representing 6 major types. Along with novel insights into the biology of individual sarcoma types, we report three overarching findings: (1) unlike most epithelial malignancies, these sarcomas (excepting synovial sarcoma) are characterized predominantly by copy-number changes, with low mutational loads and only a few genes (TP53, ATRX, RB1) highly recurrently mutated across sarcoma types; (2) within sarcoma types, genomic and regulomic diversity of driver pathways defines molecular subtypes associated with patient outcome; and (3) the immune microenvironment, inferred from DNA methylation and mRNA profiles, associates with outcome and may inform clinical trials of immune checkpoint inhibitors. Overall, this large-scale analysis reveals previously unappreciated sarcoma-type-specific changes in copy number, methylation, RNA, and protein, providing insights into refining sarcoma therapy and relationships to other cancer types.