학술논문

Concurrent Subcutaneous Panniculitis-like T-Cell Lymphoma and B-Cell Acute Lymphoblastic Leukemia in 2 Pediatric Patients.
Document Type
article
Source
Journal of pediatric hematology/oncology. 43(6)
Subject
B-Lymphocytes
CD8-Positive T-Lymphocytes
Humans
Lymphoma
T-Cell
Panniculitis
Child
Preschool
Female
Male
Precursor B-Cell Lymphoblastic Leukemia-Lymphoma
Pediatric Research Initiative
Orphan Drug
Pediatric Cancer
Rare Diseases
Childhood Leukemia
Hematology
Cancer
Lymphoma
Pediatric
Aetiology
2.1 Biological and endogenous factors
ALL
SPTCL
concurrent malignancy
immune dysregulation
clinical decision making
Cardiorespiratory Medicine and Haematology
Oncology & Carcinogenesis
Language
Abstract
Subcutaneous panniculitis-like T-cell lymphoma is a cutaneous lymphoma characterized by CD8+ T-cell infiltrate in the subcutis that is rare in children. Acute lymphoblastic lymphoma is the most common pediatric malignancy and often presents with fevers and pancytopenia. Herein, we report 2 pediatric patients presenting with subcutaneous panniculitis-like T-cell lymphoma and B-cell acute lymphoblastic lymphoma, distinct hematologic malignancies arising from different lymphoid lineages, with no identifiable germline cancer predisposition.