학술논문
Familial Congenital Hepatic Fibrosis: Report of a Family with Three Affected Children.
Document Type
Article
Author
Source
Subject
*HEPATIC fibrosis
*CONGENITAL disorders
*JUVENILE diseases
*THALASSEMIA
*DISEASE complications
*MOLECULAR biology
*MEDICAL centers
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Language
ISSN
0044-6025
Abstract
Congenital hepatic fibrosis (CHF) is a developmental disorder of the biliary system, characterized by defective remodeling of the ductal plate. Herein a family of three children, from consanguineous parents, with minor thalassemia is presented who suffered from congenital hepatic fibrosis (CHF). Prompt diagnosis and appropriate treatment are necessary to avoid further complications in the affected patients. [ABSTRACT FROM AUTHOR]