학술논문
Acute kidney injury due to thrombotic microangiopathy in a patient with primary Sjögren's syndrome.
Document Type
Article
Author
Source
Subject
*SJOGREN'S syndrome
*ACUTE kidney failure
*MONOCLONAL gammopathies
*THROMBOTIC thrombocytopenic purpura
*IMMUNOGLOBULIN producing cells
*COMPLEMENT factor H
*ANTINEUTROPHIL cytoplasmic antibodies
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Language
ISSN
0886-022X
Abstract
Two years ago, the patient's serum immunofixation electrophoresis revealed a monoclonal protein with an IgG- . Acute kidney injury due to thrombotic microangiopathy in a patient with primary Sjögren's syndrome Dear Editor, We described a case of monoclonal gammopathy-associated renal thrombotic microangiopathy (TMA) in a primary Sjögren's syndrome (pSS) patient and who was successfully treated with a bortezomib-based regimen. Her blood urea nitrogen was 18.31 mmol/L, serum creatinine (Scr) was 653 mol/L. Hypercoagulability workup revealed a high level of fibrinogen but negative anti-cardiolipin antibody immunoglobulin (Ig) G and IgM. [Extracted from the article]