학술논문

Diffuse plane xanthomatosis associated with monoclonal gammopathy
Document Type
article
Source
Anais Brasileiros de Dermatologia. August 2011 86(4)
Subject
multiple Myeloma
Paraproteinemias
Xanthomatosis
Language
English
ISSN
0365-0596
Abstract
Diffuse plane normolipemic xanthomatosis (DPNX) is a rare, non-inherited disease that is often associated with systemic diseases, mainly malignant hematological (especially multiple myeloma) or lymph proliferative disorders. The DPNX can precede the appearance of such conditions by several years, so careful follow-up and periodic laboratory examinations are recommended even for patients that seemed to have no underlying disease. We describe a case associated with monoclonal gammopathy. This case shows that dermatological lesions can be the first manifestation of important hematological diseases and so physicians should be familiarized with this entity