학술논문

Atrial Appendage Anastomosis in Hypoplastic Left Heart Syndrome With Restrictive Atrial Septum A Novel Approach
Document Type
article
Source
JACC Case Reports. 4(17)
Subject
Biomedical and Clinical Sciences
Cardiovascular Medicine and Haematology
Pediatric
Infant Mortality
Heart Disease
Cardiovascular
Rare Diseases
Good Health and Well Being
AS
aortic stenosis
ECMO
extracorporeal membrane oxygenation
EXIT
ex utero intrapartum treatment
HLHS
hypoplastic left heart syndrome
IAS
intact atrial septum
OR
operating room
atrial appendage anastomosis
hypoplastic left heart syndrome
intact atrial septum
Language
Abstract
Intact atrial septum (IAS), occurring in ∼10% of patients with hypoplastic left heart syndrome (HLHS), conveys significant neonatal morbidity and mortality. Perinatal interventions have been described, but outcomes remain poor. We present a fetus with HLHS with IAS who underwent immediate novel postnatal atrial appendage anastomosis, thus achieving rapid left atrial decompression. (Level of Difficulty: Advanced.).