학술논문

Post-acute phase and sequelae management of epidermal necrolysis: an international, multidisciplinary DELPHI-based consensus
Document Type
article
Source
Orphanet Journal of Rare Diseases. 18(1)
Subject
Biomedical and Clinical Sciences
Clinical Sciences
Dental/Oral and Craniofacial Disease
Humans
Stevens-Johnson Syndrome
Consensus
Skin
Disease Progression
Epidermal necrolysis
Stevens-Johnson syndrome
Toxic epidermal necrolysis
Sequelae
Quality of life
Delphi
Other Medical and Health Sciences
Genetics & Heredity
Genetics
Clinical sciences
Language
Abstract
BackgroundLong-term sequelae are frequent and often disabling after epidermal necrolysis (Stevens-Johnson syndrome (SJS) and toxic epidermal necrolysis (TEN)). However, consensus on the modalities of management of these sequelae is lacking.ObjectivesWe conducted an international multicentric DELPHI exercise to establish a multidisciplinary expert consensus to standardize recommendations regarding management of SJS/TEN sequelae.MethodsParticipants were sent a survey via the online tool "Survey Monkey" consisting of 54 statements organized into 8 topics: general recommendations, professionals involved, skin, oral mucosa and teeth, eyes, genital area, mental health, and allergy workup. Participants evaluated the level of appropriateness of each statement on a scale of 1 (extremely inappropriate) to 9 (extremely appropriate). Results were analyzed according to the RAND/UCLA Appropriateness Method.ResultsFifty-two healthcare professionals participated. After the first round, a consensus was obtained for 100% of 54 initially proposed statements (disagreement index