학술논문
머리띠 형태의 탈모를 동반한 패리-롬버그 증후군
Parry-Romberg Syndrome with Band-like Linear Alopecia
Parry-Romberg Syndrome with Band-like Linear Alopecia
Document Type
Article
Author
최승일 / Seung Il Choi; 양정훈 / Jung Hoon Yang; 박영립 / Young Lip Park; 이종석 / Jong Suk Lee; 황규왕 / Kyu Uang Whang; 이상훈 / Sang Hoon Lee
Source
대한피부과학회지 / Korean Journal of Dermatology. May 30, 2012 50(5):456
Subject
Language
Korean
ISSN
0494-4739
Abstract
Parry and Romberg described progressive facial hemiatrophy, characterized by progressive unilateral wasting of the skin, fat, muscle and bone in 1825 and 1846, respectively. Involvement of the central nervous system, with impairment of neurologic function, occurs infrequently. Linear scleroderma on frontal and parietal scalp, named ``en coup de sabre``, is considered an overlapping condition. An 11 year-old girl was presented to our office with left facial hemiatrophy and transverse linear band-like alopecia on her posterior parietal scalp. Histopathologically, there was a sclerotic change of the collagen fibers and dermal lymphocytic infiltrations around the skin appendages. Her skin lesion has improved by intralesional corticosteroid injection. Linear scleroderma frequently coexists with Parry-Romberg syndrome. But in this case, she had a unique pattern of scleroderma, which is distinct from the previously reported cases. (Korean J Dermatol 2012;50(5):456∼459)