부산대학교 도서관

Polysplenia syndrome is a very rare congenital disease to complicated major cardiovascular anomalies with severe cyanosis and visceral heterotaxia, in almost cases. We reported a case of choledocholithiasis with polysplenia syndrome and preduodenal portal vein and common bile duct in Tetralogy of Fallot (T/F) postoperative 16 years. In May,2000, a 56 years old woman was admitted to our hospital, because of epigastralgia after meal. Past operation histories were Blalock-Taussig operation in 34 years ago and radical operation in 16 years ago for T/F. And there were several times hospitalization for heart failure treatment. As a result of inspection after hospitalization, polysplenia, the absence of the hepatic portion of the inferior vena cava and azygos continuation of right IVC, the left-side gall bladder, intestinal malrotation, preduodenal portal vein and common bile duct were pointed out. After evaluation of a careful cardio-pulmonary function, operation was performed. We confirmed the above-mentioned anomalies and cholecystectomy and choledocholithotomy were enforced. In postoperative 14 days, she discharged uneventfully.