학술논문

Importance of Early Intracardiac Repair for Congenital Heart Disease Associated with Tracheobronchomalacia / 気管気管支軟化症を合併した先天性心疾患に対する早期心内修復術の重要性
Document Type
Journal Article
Source
日本小児循環器学会雑誌 / Pediatric Cardiology and Cardiac Surgery. 2017, 33(2):169
Subject
congenital heart disease
intracardiac repair
tetralogy of Fallot with absent pulmonary valve
tracheobronchomalacia
vascular ring
Language
Japanese
ISSN
0911-1794
2187-2988
Abstract
Result: Intracardiac repair (ICR) and division of the vascular ring improved respiratory symptoms in 9 (82%) of 11 patients. All 4 patients who did not undergo ICR died. Age at the time of surgery was I) 2.8±3.0, II) 6.0±3.4, and III) 7.8±3.9 months (mean±SD), respectively. The longest waiting period for surgery was reported for Group III (mean±SD 4.0±1.6 months). All patients in groups I and II required preoperative ventilation. Four (50%) of 8 patients with chromosomal abnormalities had poor symptom improvement.