학술논문

A case of multiple duodenal gastrointestinal stromal tumors associated with neurofibromatosis type 1 / 神経線維腫症1型に合併した多発十二指腸GISTの1例
Document Type
Journal Article
Source
日本消化器病学会雑誌 / Nippon Shokakibyo Gakkai Zasshi. 2023, 120(5):410
Subject
GIST
von Recklinghausen病
神経線維腫症1型
Language
Japanese
ISSN
0446-6586
1349-7693
Abstract
Gastrointestinal stromal tumors (GISTs) associated with von Recklinghausen's disease (neurofibromatosis type 1 [NF1]) have different pathogenesis and characteristics from common GISTs. Furthermore, no treatment strategy for this type of GIST has been established. This study presents the case of a 76-year-old man previously diagnosed with NF1 who was later diagnosed with GISTs. A resection of the horizontal leg of the duodenum was performed, and no recurrence was observed 18 months after the surgery.