학술논문

Clinical Features of Congenital Heart Disease Accompanied by Congenital Intestinal Atresia / 先天性消化管閉塞症を合併した先天性心疾患の検討
Document Type
Journal Article
Source
日本小児循環器学会雑誌 / Pediatric Cardiology and Cardiac Surgery. 2021, 37(2):117
Subject
chromosomal abnormality
congenital heart disease
congenital intestinal atresia
Language
Japanese
ISSN
0911-1794
2187-2988
Abstract
Results: CHD diagnoses included ventricular septal defect (n=22), patent ductus arteriosus (n=8), tetralogy of Fallot (n=7), and atrial septal defect (n=5). CIA included anal atresia (n=31), esophageal atresia (n=17), duodenal atresia/stenosis (n=10), and Hirschsprung’s disease (n=10). The overall survival rate of patients was 83%. Thirty-one had chromosomal abnormalities. Of those, 7 patients died. Forty patients received surgeries for both CHD and CIA consequently. In 1 patient with anal atresia, the site of stoma influenced cardiac operation. One patient with esophageal atresia underwent CIA operation after cardiac palliation for high pulmonary blood flow. One patient had duodenal obstruction associated with suture failure for high pulmonary blood flow. Three patients with Down syndrome that underwent proctostomy for Hirschsprung’s disease died from fulminant enteritis.