학술논문

Relationship Between the Tumor Resection Margin and the Clinical Course of Soft Tissue Sarcomas of the Chest Wall in Children / 小児胸壁原発軟部肉腫の根治的切除術での切除縁と臨床経過の検討
Document Type
Journal Article
Source
日本小児外科学会雑誌 / Journal of the Japanese Society of Pediatric Surgeons. 2019, 55(1):47
Subject
chest wall
children
reconstruction
resection margin
soft tissue sarcoma
切除縁
小児
胸壁
胸壁再建術
軟部肉腫
Language
Japanese
ISSN
0288-609X
2187-4247
Abstract
Results: All six patients without distant metastasis achieved disease-free survival. Three patients who underwent wide resection did not undergo radiation therapy as their initial treatment. Two patients, one with undifferentiated round cell sarcoma and a 2 cm resection margin and the other with primitive neuroectodermal tumor (PNET) and a 1 cm resection margin did not develop recurrences. However, one patient with synovial sarcoma and a 1 cm resection margin developed local recurrence. None of the three patients who underwent combined marginal resection and radiotherapy (two with PNET and one with rhabdomyosarcoma) experienced disease recurrence. Three patients underwent chest wall reconstructions without serious complications. The 5-year overall survival for all the seven patients was 85.7%, and the 5-year event-free survival was 71.4%. Only one patient with PNET who had distant metastases present at the initial visit died.