부산대학교 도서관

A 56-year-old female had a 10-year history of erythema in the periumbilical region, but left it untreated. However, when she sustained a left metatarsal fracture and visited a local orthopedic clinic, she was found to have an umbilical mass and was referred to our department. At the first examination, a 12×14.5 cm erythema in the periumbilical region and a 2.4×3.2 cm red mass in the umbilical region were noted. Visual inspection of the external genital, perianal, and axillary areas revealed no abnormalities. Skin biopsies of the periumbilical erythema and umbilical mass led to a diagnosis of solitary extramammary Paget’s disease in the umbilical region. Whole-body CT demonstrated no lymph node or visceral metastases, and the patient underwent tumor resection under general anesthesia. At present, 2 years after surgery, the patient is free from local recurrence or metastases. Few studies have reported extramammary Paget’s disease developing in the umbilical region. In Japan, 12 cases have been described, 4 of which were solitary extramammary Paget’s disease in the umbilical region. Skin Research, 19 : 1-6, 2020