학술논문
Heart Transplantation in Patients With Emery-Dreifuss Muscular Dystrophy: Case Reports
Document Type
Academic Journal
Author
Source
Transplantation Proceedings. Dec, 2007, Vol. 39 Issue 10, p3538, 3 p.
Subject
Language
English
ISSN
0041-1345
Abstract
To link to full-text access for this article, visit this link: http://dx.doi.org/10.1016/j.transproceed.2007.06.076 Byline: A. Dell'Amore, L. Botta, S. Martin Suarez, A. Lo Forte, E. Mikus, N. Camurri, L. Ortelli, G. Arpesella Abstract: Emery-Dreifuss muscular dystrophy (EDMD) is an hereditary syndrome characterized by slow but progressive locomotor involvement and cardiomyopathy. Cardiac impairment is often the life-limiting feature of the illness. Only a few cases of cardiac transplantation have been reported previously in muscular dystrophy, and only 4 cases of end-stage disease due to EDMD have been treated previously with heart transplantation. Herein we have reported our experince with 2 consecutive patients who underwent heart transplantation for EDMD cardiomyopathy. Author Affiliation: Heart and Lung Transplantation Program, S. Orsola-Malpighi University of Bologna, Bologna, Italy.