학술논문
Chylothorax and constrictive pericarditis in a woman due to generalized lymphatic anomaly: a case report
Document Type
Report
Author
Source
Journal of Cardiothoracic Surgery. June 5, 2018, Vol. 13 Issue 1
Subject
Language
English
ISSN
1749-8090
Abstract
Author(s): Hongchun Du[sup.1] , Mai Xiong[sup.2] , Huai Liao[sup.1] , Yifeng Luo[sup.1] , Huijuan Shi[sup.3] and Canmao Xie[sup.1] Background Chylothorax, the accumulation of chyle in the pleural space, can result [...]
Background Generalized lymphatic anomaly (GLA) is characterized by diffuse or multicentric proliferation of dilated lymphatic vessels resembling common lymphatic malformations. Compared with soft tissue or bone involvement, thoracic involvement may be associated with a worse prognosis. Case presentation We reported a case of GLA with chylothorax and constrictive pericarditis in a 29-year-old woman. This patient exhibited remarkable features, including a continuously hemorrhagic chylothorax, constrictive pericarditis, and involvement of bone and neck lymph nodes. After attempting to manage her condition with conservative treatment, the patient underwent pericardial stripping surgery. Exploration revealed abundant hyperplasia of tubular tissue in the aortopulmonary window in both pleural cavities. Conclusions This case highlights the importance of maintaining the clinical suspicion of GLA during the follow-up of chylothorax patients. Aggressive pericardial surgery, which is important for both diagnosis and treatment, should be performed in patients with GLA with constrictive pericarditis. Keywords: Chylothorax, Constrictive pericarditis, Generalized lymphatic anomaly
Background Generalized lymphatic anomaly (GLA) is characterized by diffuse or multicentric proliferation of dilated lymphatic vessels resembling common lymphatic malformations. Compared with soft tissue or bone involvement, thoracic involvement may be associated with a worse prognosis. Case presentation We reported a case of GLA with chylothorax and constrictive pericarditis in a 29-year-old woman. This patient exhibited remarkable features, including a continuously hemorrhagic chylothorax, constrictive pericarditis, and involvement of bone and neck lymph nodes. After attempting to manage her condition with conservative treatment, the patient underwent pericardial stripping surgery. Exploration revealed abundant hyperplasia of tubular tissue in the aortopulmonary window in both pleural cavities. Conclusions This case highlights the importance of maintaining the clinical suspicion of GLA during the follow-up of chylothorax patients. Aggressive pericardial surgery, which is important for both diagnosis and treatment, should be performed in patients with GLA with constrictive pericarditis. Keywords: Chylothorax, Constrictive pericarditis, Generalized lymphatic anomaly