학술논문

Occlusive Retinal Vasculitis in a Pediatric Patient With Kikuchi-Fujimoto Disease and Sickle Cell Trait
Document Type
Academic Journal
Source
Ophthalmic Surgery, Lasers, and Imaging Retina. February, 2024, p1, 5 p.
Subject
Massachusetts
Language
English
ISSN
2325-8160
Abstract
A 13-year-old Black male patient with a history of Kikuchi-Fujimoto disease (KFD) and sickle cell trait presented with acute painless vision loss and no light perception vision (NLP) in his left eye. The examination was indicative of occlusive retinal vasculitis with near total central retinal artery occlusion (CRAO). He was started on oral steroids with dramatic reperfusion and improvement of the retinal hemorrhages. However, his vision remained at NLP. Oral steroids were tapered, and rituximab infusion was initiated. While ocular involvement is uncommon in KFD, vision-limiting complications, such as occlusive retinal vasculitis, ophthalmic artery occlusion, and CRAO can occur. Early systemic immunosuppression is key in achieving rapid remission. [Ophthalmic Surg Lasers Imaging Retina 2024;55:XX–XX.]
Kikuchi-Fujimoto disease (KFD), first described in 1972 by two Japanese pathologists, is a self-limited disease of necrotizing lymphadenitis with histological appearance of karyorrhexis and necrosis. (1) KFD is characterized by [...]