학술논문
Safety and utility of CardioMEMS device for remote pulmonary artery monitoring in paediatric Fontan patients: a case series
CASE SERIES: Inherited cardiac conditions/cardiomyopathies
CASE SERIES: Inherited cardiac conditions/cardiomyopathies
Document Type
Academic Journal
Source
EHJ Case Reports. September 2023, Vol. 7 Issue 9
Subject
Language
English
ISSN
2514-2119
Abstract
Introduction Patients living with Fontan circulation require life-long surveillance for complications including Fontan-associated liver disease (FALD), protein-losing enteropathy (PLE), ventricular dysfunction, and plastic bronchitis. (1) Traditionally, the assessment of Fontan [...]
Background Patients with single ventricle congenital heart disease who undergo total cavo-pulmonary anastomosis (Fontan surgery) suffer from elevated pulmonary artery pressure (PAP), which leads to multiple adverse sequelae. Traditionally, the Fontan pressures are assessed via invasive haemodynamic catheterization that exposes these medically fragile patients to the risks of vascular injury and anaesthesia. While the CardioMEM remote PAP monitor has been extensively used in adults with heart failure, the safety of this device has not been established in children. Case summary We report safety and utility of this device in eight paediatric Fontan patients. Our patients ranged from 9 to 18 years of age. There were no reported complications related to the implantation of the CardioMEMS device in our population. Discussion This is the first case series of safety of CardioMEMS device in paediatric Fontan Powered by Editorial Manager[R] and ProduXion Manager[R] from Aries Systems Corporation patients. Our experience indicates that the device may be safely utilized for the management of Fontan-related complications in this vulnerable population. Keywords Fontan patients * CardioMEMs * Children * Case series ESC curriculum 9.6 Pulmonary hypertension * 9.7 Adult congenital heart
Background Patients with single ventricle congenital heart disease who undergo total cavo-pulmonary anastomosis (Fontan surgery) suffer from elevated pulmonary artery pressure (PAP), which leads to multiple adverse sequelae. Traditionally, the Fontan pressures are assessed via invasive haemodynamic catheterization that exposes these medically fragile patients to the risks of vascular injury and anaesthesia. While the CardioMEM remote PAP monitor has been extensively used in adults with heart failure, the safety of this device has not been established in children. Case summary We report safety and utility of this device in eight paediatric Fontan patients. Our patients ranged from 9 to 18 years of age. There were no reported complications related to the implantation of the CardioMEMS device in our population. Discussion This is the first case series of safety of CardioMEMS device in paediatric Fontan Powered by Editorial Manager[R] and ProduXion Manager[R] from Aries Systems Corporation patients. Our experience indicates that the device may be safely utilized for the management of Fontan-related complications in this vulnerable population. Keywords Fontan patients * CardioMEMs * Children * Case series ESC curriculum 9.6 Pulmonary hypertension * 9.7 Adult congenital heart