부산대학교 도서관

Immunoglobulin G4-related disease (IgG4-RD) is a systemic inflammatory condition with tissue infiltration of IgG4-rich plasma cells. It can present as tumefactive lesions in nearly any organ, sometimes mimicking malignancy. Lymphadenopathy is observed in some patients with IgG4-RD, and is often asymptomatic and slowly-growing. Diagnosis of IgG4-RD requires histologic confirmation, along with serologic and radiographic findings. Herein, we present a 38-year-old man who developed painless neck lymphadenopathy within weeks prior to visiting our outpatient clinic. The lymphadenopathy in our patient was first identified as lymphoma. However, the diagnosis of lgG4-RD was confirmed after repeating a lymph node biopsy.