학술논문
Irbesartan in Marfan syndrome (AIMS): a double-blind, placebo-controlled randomised trial
Document Type
Article
Author
Mullen, Michael; Jin, Xu Yu; Child, Anne; Stuart, A Graham; Dodd, Matthew; Aragon-Martin, José Antonio; Gaze, David; Kiotsekoglou, Anatoli; Yuan, Li; Hu, Jiangting; Foley, Claire; Van Dyck, Laura; Knight, Rosemary; Clayton, Tim; Swan, Lorna; Thomson, John D R; Erdem, Guliz; Crossman, David; Flather, Marcus; Dean, John; Was, Bartosz; Gow, Heather; Murray, Jane; D'Allessandro, Mariella; Christie, Michael; Cooper, Patricia; Booth, Philip; Burns, Sharon; Paterson, Yvonne; Chikermane, Ashish; Assing, Anthony; Cotter, Catherine; Atkins, Gillian; Williamson, Helen; Barclay, Justin; Jennison, Alan; Henderson, Alex; McSkeane, Anna; Fairlamb, Helen; Kelly, Julie; Kelsall, Nicola; Prentice, Scott; O'Sullivan, John; Head-Baister, Alison; Phillipson, Angela; Johnson, Anna; Crossland, D; Oliver, Jack; Davison, Jade; Wake, Jill; Quinn, Louise; Foreman, Maureen; Wealleans, Vera; Walker, Niki; Duncan, Alexis; Tibbs, Evelyn; Kelly, Ruth; Khambadkone, Sachin; Zotti, Bridget; Brady, Cassie; Cervi, Elena; Field, Ella; Szepezvary, Eszter; Mantey, Florence; Riley, Gillian; Titmus, Heather; Bo, Ilaria; Kaski, Juan Pablo; Green, Loren; Jones, Nigel; Banks, Rebecca; Kiesewetter, Christopher; Mathur, Sujeev; Frigiola, Alessandra; Savis, Alex; Belfield, Holly; Guzman, Josephine; Harris, Julia; Wilson, Karen; Peacock, Kelly; Gibson, Kirsty; Wellman, Paul; Simpson, John; Kabir, Saleha; Mushemi, Sitali; Stewart, Michael; Atkinson, Bev; Richardson, Cath; Leng, Elaine; Brennan, Paul; Nixon, Annabel; Spencer, Collette; Oliver, James; Forster, Jan; Turner, Louise; Bainbridge, Samantha; Choy, Anna Maria; Dawson, Adelle; Kiddie, Gwen; Kerr, Heather; Mordi, Ify; Duff, Jackie; Dunlop, Jacqueline; Berg, Jonathan; Armory, Pauline; Freeman, Leisa; Anwar, Amir; Graham, Charles; London, Clare; Healey, Gail; Gallagher, Ian; Ilsley, Mary; Ahmed, Rizwan; Wood, Sheila; Wheeldon, Nigel; Mason, Cecilia; Nassim, Farook; Middle, Janet; Adams, Justin; Angelini, Karen; Housley, Kay; Ryalls, Kim; Agyemang, Michael; Walker, Rachel; Batigan, Robina; Bennett, Tina; Clift, Paul; Alvior, Amor Mia; Nilsson, Annette; Green, Carole; Crook, Charlotte; Palmer, Connie Becani; Dwenger, Elizabeth; Doherty, Phillipa; Igbokwe, Rebecca; Sharif, Saba; MacDonald, Sonia; West, Cathy; Kirby, Kevin; Naqvi, Nitha; Welch, Sophie; Warsama, Suad; Li, Wei; Farzad, Zohreh; Smith, Ben; Murday, Victoria; Duncan, Alexis; Murtagh, Eamonn; Adams, Emma; Armour, Lesley; Lilley, Stuart; Pandya, Bejal; Richards, Amy; Andiapen, Mervyn; Macrae, Rebecca; Tome, Maite; Hutchinson, Carmel; Angulo, Kameka; Kauppayamootoo, Rooba; Gati, Sabiha; Cruddas, Elizabeth; Newman, William G; Breen, Catherine; Kumar, Dhavendra; Wilson, Dirk G; Farrugia, Adele; Fraser, Alan; Sumers, Jayne; Powell, Jessie; Edwards, Julie; Hale, Terese; Boult, Zoe; Carroll, Aisling; Veldtman, Gruschen; Ho, Andrew; Black, David; Fletcher, Lisa; Mapstone, Sue; Bharucha, Tara; Marsh, Gary; Jones, Joanne; Sheehan, Karen; Selway, Kathleen; Stevenson, Kirsty; Nelson, Martin; Fairweather, Rebecca; Curtis, Stephanie; Simpson, Sue; Denvir, Martin; White, Audrey; Steven, Jill; Munro, Joanna; Lam, Wayne; Toff, William; Petrou, Mario; Silcocks, Paul; MacAllister, Raymond
Source
The Lancet; December-January 2019, Vol. 394 Issue: 10216 p2263-2270, 8p
Subject
Language
ISSN
01406736; 1474547X
Abstract
Irbesartan, a long acting selective angiotensin-1 receptor inhibitor, in Marfan syndrome might reduce aortic dilatation, which is associated with dissection and rupture. We aimed to determine the effects of irbesartan on the rate of aortic dilatation in children and adults with Marfan syndrome.