학술논문

Brain monoamine vesicular transport disease caused by homozygous SLC18A2variants: A study in 42 affected individuals
Document Type
Article
Author
Saida, KenMaroofian, RezaSengoku, ToruMitani, TadahiroPagnamenta, Alistair T.Marafi, DanaZaki, Maha S.O’Brien, Thomas J.Karimiani, Ehsan GhayoorKaiyrzhanov, RauanTakizawa, MarinaOhori, SachikoLeong, Huey YinAkay, GulsenGalehdari, HamidZamani, MinaRomy, RatnaCarroll, Christopher J.Toosi, Mehran BeiraghiAshrafzadeh, FarahImannezhad, ShimaMalek, HadisAhangari, NajmehTomoum, HodaGowda, Vykuntaraju K.Srinivasan, Varunvenkat M.Murphy, DavidDominik, NataliaElbendary, Hasnaa M.Rafat, KarimaYilmaz, SanemKanmaz, SedaSerin, MineKrishnakumar, DeepaGardham, AliceMaw, AnnaRao, Tekki SreenivasaAlsubhi, SarahSrour, MyriamBuhas, DanielaJewett, TamisonGoldberg, Rachel E.Shamseldin, HananFrengen, EirikMisceo, DorianaStrømme, PetterMagliocco Ceroni, José RicardoKim, Chong AeYesil, GozdeSengenc, EsmaGuler, SerhatHull, MariamParnes, MeredAktas, DilekAnlar, BanuBayram, YavuzPehlivan, DavutPosey, Jennifer E.Alavi, ShahryarMadani Manshadi, Seyed AliAlzaidan, HamadAl-Owain, MohammadAlabdi, LamaAbdulwahab, FerdousSekiguchi, FutoshiHamanaka, KoheiFujita, AtsushiUchiyama, YuriMizuguchi, TakeshiMiyatake, SatokoMiyake, NorikoElshafie, Reem M.Salayev, KamranGuliyeva, UlviyyaAlkuraya, Fowzan S.Gleeson, Joseph G.Monaghan, Kristin G.Langley, Katherine G.Yang, HuiMotavaf, MahsaSafari, SaeidAlipour, MozhganOgata, KazuhiroBrown, André E.X.Lupski, James R.Houlden, HenryMatsumoto, Naomichi
Source
Genetics in Medicine; January 2023, Vol. 25 Issue: 1 p90-102, 13p
Subject
Language
ISSN
10983600; 15300366
Abstract
Brain monoamine vesicular transport disease is an infantile-onset movement disorder that mimics cerebral palsy. In 2013, the homozygous SLC18A2variant, p.Pro387Leu, was first reported as a cause of this rare disorder, and dopamine agonists were efficient for treating affected individuals from a single large family. To date, only 6 variants have been reported. In this study, we evaluated genotype–phenotype correlations in individuals with biallelic SLC18A2variants.