학술논문
The complex treatment paradigms for concomitant tethered cord and scoliosis: illustrative case.
Document Type
Academic Journal
Author
Fluss R; 1Department of Neurological Surgery, Montefiore Medical Center, Albert Einstein College of Medicine, Bronx, New York.; Lo Bu R; 2Dominik Purpura Department of Neuroscience, Albert Einstein College of Medicine, Bronx, New York; and.; Kobets AJ; 1Department of Neurological Surgery, Montefiore Medical Center, Albert Einstein College of Medicine, Bronx, New York.; Gomez JA; 3Department of Orthopedic Surgery, Montefiore Medical Center, Albert Einstein College of Medicine, Bronx, New York.
Source
Publisher: American Association of Neurosurgeons dba Journal of Neurosurgery Publishing Group Country of Publication: United States NLM ID: 9918227275606676 Publication Model: Electronic-Print Cited Medium: Internet ISSN: 2694-1902 (Electronic) Linking ISSN: 26941902 NLM ISO Abbreviation: J Neurosurg Case Lessons Subsets: PubMed not MEDLINE
Subject
Language
English
Abstract
Background: Scoliosis associated with tethered cord syndrome is one of the most challenging spinal deformities to manage. Multiple surgical approaches have been developed, including traditional staged and concomitant procedures, spine-shortening osteotomies, and individual vertebral column resections.
Observations: A 10-year-old female presented with congenital kyphoscoliosis with worsening curve progression, tethered spinal cord, and a history of enuresis. The scoliosis had progressed to a 26° coronal curve and 55° thoracolumbar kyphosis. Preoperative magnetic resonance imaging of the spine revealed a tethered cord between the levels of L3-4 and a large kyphotic deformity at L1. The patient underwent laminectomy, during which intraoperative motor signals were lost. A planned hemivertebrectomy at L1 was performed prior to an L4 laminectomy, untethering of the filum terminale, and posterior spinal fusion from T11 to L2. After surgery, the patient experienced transient lower-extremity weakness, with her neurological function improving from baseline over the next 2 months. Ultimately, the goal of this surgery was to halt the progressive decline in motor function, which was successfully achieved.
Lessons: Much remains to be learned about the treatment of this complicated disease, especially in the setting of concomitant scoliosis. This case serves to exemplify the complex treatment paradigms that exist when attempting to manage this clinical syndrome and that more remains to be learned.
Observations: A 10-year-old female presented with congenital kyphoscoliosis with worsening curve progression, tethered spinal cord, and a history of enuresis. The scoliosis had progressed to a 26° coronal curve and 55° thoracolumbar kyphosis. Preoperative magnetic resonance imaging of the spine revealed a tethered cord between the levels of L3-4 and a large kyphotic deformity at L1. The patient underwent laminectomy, during which intraoperative motor signals were lost. A planned hemivertebrectomy at L1 was performed prior to an L4 laminectomy, untethering of the filum terminale, and posterior spinal fusion from T11 to L2. After surgery, the patient experienced transient lower-extremity weakness, with her neurological function improving from baseline over the next 2 months. Ultimately, the goal of this surgery was to halt the progressive decline in motor function, which was successfully achieved.
Lessons: Much remains to be learned about the treatment of this complicated disease, especially in the setting of concomitant scoliosis. This case serves to exemplify the complex treatment paradigms that exist when attempting to manage this clinical syndrome and that more remains to be learned.