학술논문
Severe Aortic Valvular Incompetence From IgG4-Related Disease: An Unusual Entity.
Document Type
Report
Author
Soh BWT; Department of Cardiology, University Hospital Limerick, Limerick, Ireland.; Prendergast SC; Department of Histopathology, Cork University Hospital, Cork, Ireland.; Burke L; Department of Histopathology, Cork University Hospital, Cork, Ireland.; O'Connor CT; Department of Cardiology, University Hospital Limerick, Limerick, Ireland.; Ullah I; Department of Cardiology, University Hospital Limerick, Limerick, Ireland.; O'Brien JM; Department of Radiology, University Hospital Limerick, Limerick, Ireland.; Hinchion JA; Department of Cardiothoracic Surgery, Cork University Hospital, Cork, Ireland.; Arnous S; Department of Cardiology, University Hospital Limerick, Limerick, Ireland.; Kiernan TJ; Department of Cardiology, University Hospital Limerick, Limerick, Ireland.; School of Medicine, University of Limerick, Limerick, Ireland.
Source
Publisher: Elsevier Inc Country of Publication: Netherlands NLM ID: 101757292 Publication Model: eCollection Cited Medium: Internet ISSN: 2666-0849 (Electronic) Linking ISSN: 26660849 NLM ISO Abbreviation: JACC Case Rep Subsets: PubMed not MEDLINE
Subject
Language
English
Abstract
IgG4-related disease (IgG4-RD) is a new clinical entity characterized by lymphoplasmacytic lesions rich in IgG4-positive plasma cells. Myocardial involvement is extremely rare and not a typical cardiovascular manifestation of IgG4-RD. We report a rare case of IgG4-RD-associated myocardial mass causing severe aortic incompetence, successfully treated with surgery and corticosteroids. ( Level of Difficulty: Intermediate. ).
Competing Interests: The authors have reported that they have no relationships relevant to the contents of this paper to disclose.
(© 2023 The Authors.)
Competing Interests: The authors have reported that they have no relationships relevant to the contents of this paper to disclose.
(© 2023 The Authors.)