학술논문
Morphological progression of biphenotypic sinonasal sarcoma to high‐grade sarcoma at 7 years from onset.
Document Type
Article
Source
Subject
*SARCOMA
*SOFT tissue tumors
*SYNOVIOMA
*PARANASAL sinuses
*ETHMOID bone
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Language
ISSN
0309-0167
Abstract
In summary, although BPSS displays a spindle cell morphology that often mimics other soft tissue tumours (synovial sarcoma, spindle cell/sclerosing rhabdomyosarcoma and MPNST), its dual immunohistochemical profile, together with a distinctive genetic alteration and an indolent clinical course, sets BPSS as a distinctive entity. I Sir i : Biphenotypic sinonasal sarcoma (BPSS) is an exceedingly rare, locally aggressive spindle cell soft tissue neoplasm with high trophism for the sinonasal tract of middle-aged adults, with female predilection. Keywords: biphenotypic sinonasal sarcoma; high-grade sarcoma; MAML3; PAX3; progression; sinonasal tumour EN biphenotypic sinonasal sarcoma high-grade sarcoma MAML3 PAX3 progression sinonasal tumour 825 826 2 10/06/23 20231101 NES 231101 Data availability statement Data sharing not applicable to this article, as no data sets were generated or analysed during the current study. [Extracted from the article]