학술논문

Intraoral Desmoplastic Fibroma: A Manifestation of Tuberous Sclerosis.
Document Type
Article
Source
Fetal & Pediatric Pathology. Aug2012, Vol. 31 Issue 4, p195-201. 7p.
Subject
*SOFT tissue tumors
*TUBEROUS sclerosis diagnosis
*ORAL cancer diagnosis
*CHILDHOOD cancer
*PEDIATRIC neurology
*MAXILLA
BONE tumor diagnosis
Language
ISSN
1551-3815
Abstract
Desmoplastic fibroma (DF) is a benign but locally aggressive tumor usually recognized as an intraosseous counterpart of soft tissue fibromatosis in both gnathic and extra-gnathic sites. The most common site is mandible followed by pelvis and long bones. Maxilla has been reported to be involved very rarely. Desmoplastic fibroma is recently being considered to be one of the oral manifestations of tuberous sclerosis rather than a coincidental finding. We report an unusual case of a girl with a previous diagnosis of tuberosclerosis who presented at 8 years with an oral lesion diagnosed as desmoplastic fibroma. [ABSTRACT FROM AUTHOR]