부산대학교 도서관

To the Editor: Chronic granulomatous disease (CGD) is an inborn error of immunity characterized by defects in the NADPH oxidase machinery, which is required for the production of reactive oxygen species (ROS) that aid in clearance of certain bacteria and fungi. E CT chest 27 months after his initial presentation that shows clear lungs with post-surgical changes from prior open lung biopsy He was treated with 2 mg/kg of IV methylprednisolone for 14 days followed by a taper over 2 weeks. Manifestation of inflammation in the lung includes non-infectious granulomatous inflammation, micronodules, fibrosis, and interstitial lung disease. D CT chest 6 months after the patient's initial presentation when he had recurrence of pulmonary hypertension in the setting of histoplasmosis reactivation. [Extracted from the article]