학술논문
World's smallest combined en bloc liver‐pancreas transplantation.
Document Type
Case Study
Author
Source
Subject
*PANCREAS transplantation
*COMPLICATIONS from organ transplantation
*AUTOSOMAL recessive polycystic kidney
*TRANSPLANTATION of organs, tissues, etc. in children
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Language
ISSN
1397-3142
Abstract
Abstract: We present a case of a 2‐year‐old child who underwent a combined en bloc liver and pancreas transplant following complications of WRS. WRS is characterized clinically through infantile insulin‐dependent diabetes mellitus, neutropenia, recurrent infections, propensity for liver failure following viral infections, bone dysplasia, and developmental delay. Usually, death occurs from fulminant liver and concomitant kidney failure. Few cases with WRS are reported in the literature, mostly from consanguineous parents. To the best of our knowledge, combined en bloc liver and pancreas transplant has not been performed in small children. [ABSTRACT FROM AUTHOR]