학술논문
A nationwide study evaluating the association of autoimmune bullous diseases and acquired haemophilia: description of clinical and prognostic features.
Document Type
Article
Author
Source
Subject
*BULLOUS pemphigoid
*AUTOIMMUNE diseases
*HEMOPHILIA
*HEALTH facilities
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Language
ISSN
0007-0963
Abstract
When the clinical manifestations of AHA appeared, six patients had active AIBD, three had AIBD controlled with topical steroids and one had AIBD in partial remission under methotrexate and oral steroids. HB of the oropharynx as an early sign of AHA in AIBD patients have been reported in case reports.3 Rituximab can be effective for both diseases. Dear Editor, Acquired haemophilia A (AHA) is a bleeding disorder caused by neutralizing autoantibodies targeting factor VIII (FVIII).1 AHA has been rarely associated with autoimmune bullous diseases (AIBD).1 The aim of this study was to describe the specific clinical, immunological and prognostic features of patients with an AIBD and secondary AHA. [Extracted from the article]