부산대학교 도서관

Gorham's syndrome is a rare osteolytic disease in which progressive and spontaneous resorption of bone occurs. We present a case of a boy who presented with Chiari I malformation and recurrent meningitis without fistula. The patient was submitted to occipital bone biopsy and due to lymphocytic infiltration and intraosseous vascular ectasia the diagnosis of Gorham-Stout Syndrome was made. The patient underwent conservative treatment but, unfortunately he died by cardiorespiratory arrest secondary to atlantooccipital dislocation. This case emphasizes the rarity of this pathology and the previously unreported association with recurrent meningitis without fistula. [ABSTRACT FROM AUTHOR]