부산대학교 도서관

Cystic fibrosis (CF) is the most common potentially lethal genetic disease in the white population. Improvements in life expectancy have led to an increasing recognition of hepatobiliary complications from CF. Splenic artery aneurysms are a rare complication of portal hypertension with a high mortality due to their significant potential for rupture, resulting in life-threatening i.p. haemorrhage. The optimum treatment of ruptured splenic artery aneurysms is controversial. This case describes the successful emergency embolization of multiple splenic artery pseudoaneurysms associated with portal hypertension complicating cystic fibrosis.