학술논문
Portopulmonary hypertension: Success with combined medical treatment
Document Type
article
Author
Source
Respirology Case Reports, Vol 11, Iss 4, Pp n/a-n/a (2023)
Subject
Language
English
ISSN
2051-3380
Abstract
Abstract Portopulmonary hypertension is an uncommon disease associated with high morbidity and mortality, so its early diagnosis and treatment are essential. We report here the case of a 57‐year‐old man with portopulmonary hypertension caused by chronic hepatosplenic schistosomiasis and also liver cirrhosis due to hepatitis C and alcoholism. As well as treating both diseases, portopulmonary hypertension was successfully managed with tadalafil and macitentan as maintenance therapy. This case reminds clinicians that pulmonary hypertension can be multifactorial, a good diagnosis and a multidisciplinary treatment can lead to improved prognosis.