부산대학교 도서관

This article discusses a rare presentation of osteogenesis imperfecta (OI), also known as brittle bone disease or "glass bone disease." OI is a genetic disorder that affects the production of collagen, leading to fragile and easily fractured bones. The article describes the case of a 7-year-old male child with OI type IV who presented with old malunited femur fracture, bony deformity, and multiple fractures without a history of trauma. The child was treated with intravenous zoledronate and planned for surgical intervention involving multiple osteotomies and medullary nail fixation. The article also mentions the use of the Fassier-Duval telescoping rod to prevent fractures and correct deformities in children with OI. [Extracted from the article]