학술논문
Scimitar syndrome, bronchiectasis, haemoptysis and a pneumonectomy.
Document Type
Report
Author
Jeffs E; Department of Respiratory Medicine Te Whatu Ora Waitaha Canterbury Pānui Christchurch New Zealand.; Lee H; Department of Radiology Te Whatu Ora Waitaha Canterbury Pānui Christchurch Canterbury New Zealand.; Beckert L; Department of Respiratory Medicine Te Whatu Ora Waitaha Canterbury Pānui Christchurch New Zealand.
Source
Publisher: John Wiley & Sons, Inc Country of Publication: United States NLM ID: 101631052 Publication Model: eCollection Cited Medium: Print ISSN: 2051-3380 (Print) Linking ISSN: 20513380 NLM ISO Abbreviation: Respirol Case Rep Subsets: PubMed not MEDLINE
Subject
Language
English
ISSN
2051-3380
Abstract
Scimitar syndrome is a rare condition characterized by partial or complete anomalous pulmonary venous drainage of the lung to the inferior vena cava, right lung hypoplasia and dextroposition of the heart. Haemoptysis is uncommon in adults, although the clinical spectrum is wide. We report a case of a 38-year-old male with scimitar syndrome who had low grade haemoptysis persisting over several years secondary to bronchiectatic changes in his hypoplastic right lung. Conservative measures to manage haemoptysis were unsuccessful and the patient proceeded to bronchial artery embolization. The post-procedure course was complicated by lung infarction and the patient ultimately required pneumonectomy. Deformities of the blood vessels and lungs are complex in scimitar syndrome. Bronchial artery embolization should be approached cautiously to protect pulmonary perfusion.
Competing Interests: None declared.
(© 2023 The Authors. Respirology Case Reports published by John Wiley & Sons Australia, Ltd on behalf of The Asian Pacific Society of Respirology.)
Competing Interests: None declared.
(© 2023 The Authors. Respirology Case Reports published by John Wiley & Sons Australia, Ltd on behalf of The Asian Pacific Society of Respirology.)